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1.
Iranian Journal of Dermatology. 2008; 11 (2): 93-94
em Inglês | IMEMR | ID: emr-87067
2.
Iranian Journal of Dermatology. 2005; 8 (2): 145-148
em Persa | IMEMR | ID: emr-71253

RESUMO

Mal de Meleda [keratoderma palmoplantaris transgrediens] is a rare autosomal recessive form of palmoplantar keratoderma with hyperkeratosis of palms and soles, which appears soon after birth and progressively involves other areas [transgrediens] of the skin especially dorsal aspects of hands and feet. We report a 20-year-old woman with Mal de Meleda with some unusual clinical features, i.e. peculiar finger nail anomalies and pseudoainhum on all her fingers


Assuntos
Humanos , Feminino , Ceratodermia Palmar e Plantar/etiologia , Ceratodermia Palmar e Plantar/genética , Hiperceratose Epidermolítica , Unhas Malformadas
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