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Artigo em Inglês | IMSEAR | ID: sea-94883

RESUMO

Double Orifice Mitral Valve (DOMV) is a rare congenital abnormality. Reports of 4 patients with DOMV are presented. As associated anomalies, one had ostium primum atrial septal defect (ASD). Second one had Ebstein's anomaly. Third one had grade IV tricuspid regurgitation, thickened tricuspid valve and right atrial mass. Fourth one had sinus venosus ASD. Echocardiography is the gold standard investigation. Surgical treatment depends upon the mitral valve function and associated anomalies.


Assuntos
Adolescente , Adulto , Anomalia de Ebstein/complicações , Ecocardiografia , Feminino , Sopros Cardíacos/etiologia , Comunicação Interatrial/complicações , Humanos , Masculino , Valva Mitral/anormalidades , Insuficiência da Valva Tricúspide/complicações
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