RESUMO
Psammomatoid juvenile ossifying fibroma (PsJOF) is a well defined clinical and histological entity with earlier onset at (childhood or adolescence) classified under the broad category of fibro-osseous lesion. Histological PsJOF is one of the entity of juvenile ossifying fibroma (JOF) characterized by small spherical ossicles resembling psammoma bodies and the other with trabecular or fibrillar osteoid and woven bone which is termed as trabecular juvenile ossifying fibroma (TrJOF). This case of PsJOF involved maxilla, premaxilla, antrum, lateral wall of nose on left side of face. The size, extent and aggressive behavior of the tumor which has lead to facial disfigurement and difficulty in breathing, inability to speak, eat and drink is rare in literature. The treatment done by resection with safe margins is adequate with no recurrence as patient is under follow up for more than one year.