RESUMO
Budd-Chiari syndrome is an uncommon disorder, and it is caused by obstruction of the hepatic venous outflow or inferior vena cava above the hepatic vein. It may result from a large number of conditions, including primary congenital obstructions of the hepatic veins or inferior vena cava by webs or bands. Secondary causes include trauma, polycythemia vera, chronic leukemia, pregnancy, tumors and use of oral contraceptives. No definitive etiologic factors have been identified in two thirds of all cases (1-3). We recently experienced a case of Budd-Chiari syndrome caused by diaphragmatic hernia in 21-year-old man. Postoperative follow up CT showed normal venous flow after reintroduction of the liver into the abdominal cavity and closure of the diaphragm defect.
Assuntos
Humanos , Gravidez , Adulto Jovem , Cavidade Abdominal , Síndrome de Budd-Chiari , Anticoncepcionais Orais , Diafragma , Seguimentos , Veias Hepáticas , Hérnia , Hérnia Diafragmática , Leucemia , Fígado , Policitemia Vera , Veia Cava InferiorRESUMO
Budd-Chiari syndrome is an uncommon disorder, and it is caused by obstruction of the hepatic venous outflow or inferior vena cava above the hepatic vein. It may result from a large number of conditions, including primary congenital obstructions of the hepatic veins or inferior vena cava by webs or bands. Secondary causes include trauma, polycythemia vera, chronic leukemia, pregnancy, tumors and use of oral contraceptives. No definitive etiologic factors have been identified in two thirds of all cases (1-3). We recently experienced a case of Budd-Chiari syndrome caused by diaphragmatic hernia in 21-year-old man. Postoperative follow up CT showed normal venous flow after reintroduction of the liver into the abdominal cavity and closure of the diaphragm defect.