RESUMO
Pulmonary arterial hypertension(PAH)is the most common complication of congenital heart disease (CHD). Because of the complexity and diversity of cardiac anatomy and pathophysiology,as well as a variety of adap-tive mechanisms that are not fully understood,little attention is paid on pulmonary arterial hypertension associated with congenital heart disease(CHD-PAH). This article aims to summarize the clinical status,disease characteristics,out-comes,and prognosis of CHD -PAH in Pediatric Cardiology,Beijing Anzhen Hospital,proposing current unresolved issues and future challenges.
RESUMO
Pulmonary arterial hypertension(PAH) is the most common complication of congenital heart disease(CHD). Because of the complexity and diversity of cardiac anatomy and pathophysiology, as well as a variety of adaptive mechanisms that are not fully understood, little attention is paid on pulmonary arterial hypertension associated with congenital heart disease(CHD-PAH). This article aims to summarize the clinical status, disease characteristics, outcomes, and prognosis of CHD-PAH in Pediatric Cardiology, Beijing Anzhen Hospital, proposing current unresolved issues and future challenges.