RESUMO
RESUMEN El liquen plano es una enfermedad inflamatoria de etiología multifactorial y en ocasiones desconocida, con múltiples variedades clínicas. La entidad lineal fue descrita por primera vez en 1917 y recién en1993, se le nombra variedad lineal blaschkoide. Es más frecuente su aparición en la población infantil, siendo de interés conocer la asociación de esta distribución inusual y su desencadenante en pacientes pediátricos.Se trata de una paciente con cuadro clínico de cuatro años de evolución,presentando máculas hiperpigmentadas en la línea media de la cara interna de la raíz del muslo izquierdo, característicamente, han tenido una extensión lineal y en los seis últimos meses alcanzaningle y labio mayor ipsilateral.
SUMMARY Lichen planus is an inflammatory disease of multifactorial and sometimes unknown etiology, with multiple clinical varieties. The linear entity was first described in 1917, but it was not until 1993 that it received the name of Blaschkoid linear variety. More frequently seen among children, it is of particular interest its association with congenital syndromes and the environmental triggers involved in its pathogenesis. We present a 9-year-old female patient with a clinical picture of 4 years of evolution consisting of hyperpigmented macules on the left proximal medial thigh, which characteristically have had a linear distribution and in the last 6 months have spread into the groin and ipsilateral major lip.
RESUMO
Background: Segmental vitiligo is a small but unique subset of vitiligo requiring due importance due to its lack of response to medical treatment but excellent response to surgical treatment. Characterization of the pattern of segmental vitiligo will also help to understand the pathogenesis of the disease. Aim: To characterize clinically the features of segmental vitiligo, a cross-sectional clinical study at dermatology outpatient department at AIIMS was carried out. Methods: Consecutive 188 patients were evaluated to characterize the clinical features of segmental vitiligo by detailed history, clinical examination, and photography. Frequency of each clinical feature was calculated. Results: Certain features such as early onset, initial progression of disease followed by stability, blaschkoid pattern, irregular margins, leucotrichia within and beyond the vitiligo lesion, and islands of pigmented macules within the vitiligo lesion were found to be characteristic of the disease. Conclusions: A combination of various features such as early onset of disease, blaschkoid pattern, irregular margins, leucotrichia, and islands of pigmented macules within the vitiligo lesion are helpful in diagnosis of the disease.
RESUMO
Eccrine spiradenoma (ES) very rarely presents in a linear or zosteriform distribution. It may be associated with foci of various other appendageal tumors. We report a 14-year-old boy who presented to us with multiple nodules in a linear distribution in the posterior aspect of the right lower limb since 2 years of age. The lesions became significantly painful for the past 2 years. Histopathology revealed dermal lobules of ES with smaller foci of chondroid syringoma.