Histiocitosis de células de Langerhans ósea a forma poliostótica.A propósito de un caso / Histiocytosis of Langerhans cells bone to polyostotic form. A case report

RESUMEN Se presenta el caso de un paciente masculino de 39 años de edad, con antecedentes de buena salud aparente que fue ingresado en la sala de clínica oncológica, por presentar dolores articulares en región costal, cervical y lumbo sacra que le dificultaban la marcha, además de notar un aumento de volumen en la región lateral derecha de la frente. En inicio se admite con diagnóstico de mieloma múltiple y compresión medular para recibir tratamiento con radioterapia. Los estudios imagenlógicos, histopatológicos e inmunohistoquìmicos confirmaron la histiocitosis de langerhans ósea a forma poliostótica.

ABSTRACT A case of a 39-year-old male patient is presented with a history of good apparent health who was admitted to the oncology clinic, due to articular pain in the costal, cervical and lumbar sacral regions that made walking difficult. In addition, It was noticed an increase in volume in the right lateral region of the forehead. Initially, he was admitted with a diagnosis of multiple myeloma and spinal cord compression to receive treatment with radiotherapy. Imaging, histo-pathological and immune-histo-chemical studies confirmed the histio-cytosis of bone langerhans to a polyostotic form.

Torcicolo agudo como manifestação clínica isolada de histiocitose / Acute torticollis as a single clinical manifestation of histiocitosis

Menino, com 9 anos de idade, teve episódio agudo prolongado de torcicolo (laterocólis à esquerda), com duração de quinze dias. Radiografia de coluna evidenciou colapso da vértebra C5 e o diagnóstico final foi granuloma eosinofílico. O torcicolo pode ser agudo, recorrente ou prolongado. No adulto, a maioria dos casos de torcicolo recorrente é postural, mas na infância, torcicolos recorrentes ou prolongados tiveram possibilidade significativamente aumentada de haver uma causa, sendo asmais comuns lesões estruturais de coluna e lesões de neurônio motor primário.

A 9-year old boy presented an acute episode of torticollis (left deviation) that lasted for fifteen days. Conventional radiology of the cervical spine showed collapse of the C5 vertebra. His conclusive diagnosis was thatof eosinophilic granuloma. Torticollis can be acute recurrent or prolonged. In adulthood, most cases of recurrent torticollis are caused by postural problems; however, in childhood, recurrent or prolonged torticollis is much more likely to have a cause, and the most common are spine structural lesions or lesions in the primary motor neuron.