RESUMO
RESUMEN La müllerianosis es una enfermedad embrionaria de los conductos de Müller o paramesonéfricos, que consiste en la mezcla de dos o más tipos de tejidos y que da como resultado la formación de adenomiosis, endometriosis, endosalpingiosis y endocervicosis. Con mayor frecuencia afecta la vejiga urinaria de las mujeres en edad fértil. La müllerianosis del cuello uterino es una afección benigna muy rara, con pocos casos reportados. La patogenia exacta sigue siendo tema de debate. Existen varias teorías sobre su etiología; las dos principales son la teoría de implantación y la metaplásica. Los síntomas varían desde su ausencia hasta dolor pélvico y dismenorrea. Generalmente aparece como tumor quístico con glándulas de diferentes tamaños revestidas por epitelio endometrial, endocervical o tubárico. Esta lesión podría confundirse con otras lesiones benignas, premalignas o malignas y es necesario la confirmación histopatológica. Debido a que es una enfermedad benigna, no necesita tratamiento adicional luego de la resección quirúrgica. Se presenta un caso de müllerianosis del cuello uterino.
ABSTRACT Müllerianosis is an embryonal disease of the müllerian or paramesonephric ducts, consists in the mixture of two or more types of tissues and results in the formation of adenomyosis, endometriosis, endosalpingiosis, and endocervicosis. It most often affects the urinary bladder in women of childbearing age. Müllerianosis of the cervix is a very rare benign condition, with few reported cases. The exact pathogenesis remains a matter of debate. There are several theories on its etiology; the main two are the implantation and metaplastic theories. Symptoms range from absent to pelvic pain and dysmenorrhea. It generally appears as a cystic tumor with glands of different sizes lined by endometrial, endocervical, or tubal epithelium. This lesion could be confused with other benign, premalignant, or even malignant lesions, and histopathological confirmation is necessary. Because it is a benign disease, no additional treatment is required after surgical resection. A case of müllerianosis of cervix is presented.
RESUMO
Müllerianosis is an embryonic Müllerian disease, resulting in the formation of the benign diseases adenomyosis, endometriosis, endosalpingiosis, and endocervicosis. Endocervicosis primarily affects the bladder, and rarely the cervix. Cervical endocervicosis, which is also a pseudoneoplastic glandular lesion, could be misinterpreted as a premalignant or even a malignant lesion. Because the treatment of these diseases is very different, early clinical diagnosis is important. Unfortunately, however, this lesion is difficult to diagnose preoperatively using clinical and radiological information, and pathological confirmation is needed. Herein, we report a rare case of cervical endocervicosis that was difficult to diagnosis preoperatively.