Expert Consensus on Assessment for Rehabilitation and Treatment of Musculoskeletal Complications of Hemophilia in China / 罕见病研究

@#Hemophilia is a group of hereditary hemorrhagic diseases. Hemorrhages mostly occur in musculoskeletal system and is the main cause for disability. Rehabilitation plays an important role in the comprehensive management in hemophilia. In recent years, researches on rehabilitative assessment and treatment of hemophilia have made a lot of progress in China. Using evidence-based method, experts from different disciplines have reached a consensus on the rehabilitation assessment and treatment of hemophilia skeletal muscle complications, providing an important reference to the clinical practice.

Eosinophilic Fasciitis and Musculoskeletal Complication in a Child : A case report

Eosinophilic fasciitis (EF) in childhood is a very rare, and it is characterized by diffuse fasciitis and peripheral eosinophilia. It has been reported that EF shows good recovery after systemic steroids. We report a case of 18 months old boy with eosinophilic fasciitis which affected the right lower extremity and flank. The case we present here differs from other published reports, in that the patient with eosinophilic fasciitis presented serious musculoskeletal complications such as muscle atrophy, osteoporosis, fracture, and inequality of limb length that were associated with chronic course of steroids therapy. Interdisciplinary approach is critical in preventing complications in children with eosinophilic fasciitis.

The Prospectives on The Association between Disability Resulted from Hansen's Disease and Orthosis Prescribed to Patients with Hansen's Disease / 나학회지

BACKGROUND: Hansen's disease is chronic disease, often resulting in musculoskeletal complication such as chronic ulcer, deformity, disability. The aim of this article is to know the present status of prescription of orthosis and to assess the usefulness of orthosis. METHODS: Analysis was done on subjects who had were prescribed orthosis from December, 2007 to November, 2008 at the Clinic of Reserch Center. We have asked the patients questionnaire such as frequency of use of the prescribed orhtosis, the degree of pain reduction and comfortability with orthosis,the cause of disuse of orthosis ,the degree of preventing relapse of ulcer with orthosis, request about prescribed orthosis. RESULTS: The total number who were prescribed orthosis was 173. About 69.4% patients have used orthosis very frequently or nearly at all times. About 83.2% patients said that orthosis had done them good in pain reduction, preventing relapse of ulcer. The major reason of disuse of orthosis was inconvenience of management, not no-helfulness. The major request about orthosis were improvement of quality, imprvement of strength of orthosis, shortening of limitation term of prescription. CONCLUSINON: The prescription of orthosis to Hansen patients with musculoskeletal sequale improve quality of life and is available in preventing relapse of ulcer.