RESUMO
Las fisuras oblicuas faciales son anormalidades poco frecuentes, aunque la incidencia exacta es desconocida, se reporta una incidencia de 1.5 a 5 por 100,000 nacimientos. Tessier en 1976 propuso una clasificación de las fisuras faciales, craneofaciales y laterofaciales. Morian describió la fisura oral nasoorbitaria (fisura número 3), que representa una de las malformaciones más difíciles de corregir para el cirujano plástico y reconstructivo. Reportamos un caso de fisura craneofacial Tessier número 3 así como la técnica de corrección quirúrgica empleada. Los autores enfatizan en el análisis de la embriología facial.
The oblique facial clefts are extremely rare facial anomalies, although the exact incidence of these facial clefts is unknown, is reported an incidence de 1.5 to 5 per 100,000 births. Tessier in 1976 proposed an anatomic classification of the facial, craniofacial, and laterofacial clefts. Number 3 clefts o oral-nasal-ocular cleft was described by Morian and represents one of the most difficult malformations to correct for the reconstructive surgeon. We report a case of unilateral Tessier No 3 craniofacial cleft and our approach to surgical correction. The authors emphasize in the analysis of the facial embryology.
RESUMO
PURPOSE: To report a single case of surgical repair of the canalicular defects and congenital eyelid colobomas associated with Tessier No. 3 craniofacial cleft. CASE SUMMARY: A one-month-old girl presented with eyelid colobomas and discharges from the eyes. The patient was diagnosed with a Tessier No. 3 craniofacial cleft with bilateral lower eyelid colobomas medial to the puncta. At the age of 55 months, examination under general anesthesia revealed mid-canalicular obstructions in both lower canaliculi. After pentagonal excision of eyelid colobomas in the left upper and both lower eyelids, both ends of the canaliculi were found at the cut edge of the lower eyelids. After the repair of canalicular defects and bilateral nasolacrimal duct silicone tube intubation, the primary closure of the eyelid defect was performed layer by layer. Although there was no subjective improvement of epiphora in the left eye, a subjective improvement of epiphora in the right eye was achieved, and tear meniscus height in the right eye was halved. Additionally, the eyelid colobomas were cosmetically well repaired at postoperative 6 weeks. The patient still had mild tearing symptoms, but did not complain any longer of discharge at postoperative 4 months. CONCLUSIONS: Tessier No. 3 craniofacial cleft with eyelid colobomas can be associated with canalicular defects and nasolacrimal duct obstructions. Surgical repair of the canalicular defects associated with eyelid colobomas should be considered to achieve a functional recovery of the lacrimal drainage system.