Papillon–Lefevre Syndrome: A Case Report with Review of Literature

Papillon–Lefevre Syndrome(PLS) is a very rare syndrome of autosomal recessive inheritance characterised by palmar plantar hyperkeratosis and early onset of a severe destructive periodontitis, leading to premature loss of both primary and permanent dentitions. The palmar plantar keratoderma typically has its onset between the ages of 1 and 4 years and severe periodontitis starts at the age of 3 or 4 years. The exact pathogenesis of these clinical events remains mainly speculative. An early diagnosis of the syndrome can help preserve the teeth by early institution of treatment, using a multidisciplinary approach. We report a case of 17-year- old female patient with PLS.

Natal tooth: A Case Report and Review.

Natal teeth are defined as teeth that are present in the mouth at the time of birth. It must be considered that natal and neonatal teeth are conditions of fundamental importance not only for a dental surgeon but also for a paediatrician, since their presence may lead to numerous complications. Hence the purpose of the present paper is to review and discuss its clinical features, complications and management.