Carcinome adénoïde kystique de la fosse nasale : à propos d'un cas et revue de littérature

Parmi les tumeurs de la tête et du cou, le carcinome adénoïde kystique ne représenteque 1%. C'est la tumeur maligne la plus fréquente des glandes salivaires accessoires.Sa localisation dans la fosse nasale est exceptionnelle. Nous rapportons un cas de carcinome adénoïde kystique de la fosse nasale chez une patiente de 42 ans qui se présente pour une symptomatologie nasale. La tomodensitométrie objective un processus tissulaire de la fosse nasale droite, l'endoscopie montre une tumeur s'étendant au vestibule avec à la biopsie un carcinome adénoïde kystique. La prise en charge chirurgicale a consisté en une exérèse de la tumeur avec maxillectomie totale suivie d'une radiothérapie

Carcinoma adenoideo quístico / Adenoid cystic carcinoma

El carcinoma adenoide quístico representa aproximadamente un 25 por ciento de los tumores de cabeza y cuello, ubicado principalmente a nivel de paladar, labio y mucosa bucal. Mantiene un curso lento pero con probabilidad de metástasis a largo plazo con diseminación de predominio vascular y raramente a nódulos linfáticos. Clínicamente se manifiesta como indolente manifestado principalmente como una masa. El método diagnóstico más importante es el examen físico con exámenes complementarios por medio de ultrasonido y dependiendo de características propias de la masa se solicitar resonancia magnética para delimitar patología como guía durante procedimiento quirúrgico. Como tratamiento de primera línea se utiliza la resección quirúrgica y se ha demostrado mejores resultados con la agregación de radioterapia.

Carcinoma adenoide quístico primario de bronquio lobar: caso clínico / Primary adenoid cystic carcinoma of the lobar bronehus: case report

Primary airway adenoid cystic carcinoma is very uncommon. We report a 60 years old male consulting for hemoptysis and dyspnea. A chest CAT scan showed a mass in the right superior lobar bronehus. The patient was subjected to a right superior sleeve lobectomy and the pathological study of the surgical piece revealed an adenoid cystic carcinoma. The patient received adjuvant radiotherapy. Surgery and radiation therapy are the mainstay of treatment for this type of tumors.

El carcinoma adenoide quístico primario de la vía aérea es una neoplasia muy rara. Reportamos el caso de un paciente de 60 años de edad quien consultó por hemoptisis y disnea de esfuerzo. Una tomografía computarizada del tórax reveló una masa en el bronquio fuente y lobar superior del pulmón derecho. Se realizó una lobectomía superior derecha en manguito. El estudio histopatológico mostró un carcinoma adenoide quístico. Se administró radioterapia adyuvante. La cirugía y la radioterapia son las bases del manejo de este tipo de tumores.

Les carcinomes adenoides kystiques de la parotide a propos de 3 cas

Les carcinomes adenoides kystiques (CAK) representent 2 a 4des tumeurs de la parotide et 12des tumeurs malignes. Ce sont des tumeurs a croissance lente qui sont caracterisees par leur capacite a infiltrer les gaines nerveuses. Les auteurs rapportent trois cas de CAK de la glande parotide diagnostiques et traites entre l'annee 2000 et 2007. Il s'agissait de 2 hommes et une femme qui ont consulte devant l'apparition d'une tumefaction de la loge parotidienne associee a une paralysie faciale dans un cas. Les aires ganglionnaires etaient libres. Tous les patients ont beneficie d'une exploration comportant une echographie; une TDM dans un cas et une IRM chez un patient. Le traitement a consiste en une parotidectomie totale associee a un curage ganglionnaire dans tous les cas et a une radiotherapie complementaire. L'evolution a ete favorable dans deux cas. Le carcinome adenoide kystique de la parotide est une tumeur rare; caracterisee par une evolution tres lente; une agressivite locale; un caractere fortement recidivant localement et un haut pouvoir metastatique a distance

Adenoid cystic carcinoma of the trachea

Primary malignant neoplasms of the trachea are very rare and there is limited information available on this subject. Adenoid cystic carcinoma is a slow-growing malignant tracheal tumor and the best method of treatment is surgical resection. This study was conducted to evaluate patients with adenoid cystic carcinoma of the trachea who underwent surgical treatment. In this descriptive study, 9 patients treated for adenoid cystic carcinoma from 1995 to 2007 at the Mashhad Ghaem Hospital and Tehran Imam Khomeini Hospital were assessed. There were 9 patients [3 males and 6 females] with a mean age of 56.3 years. Dyspena and stridor were the most common presenting symptoms [88.8%]. All patients underwent rigid bronchoscopy and biopsy. The most common site of involvement was the lower third of trachea [44.4%]; 77.7% of patients underwent surgical resection. Death occurred in one patient after tracheal resection due to aspiration pneumonia [14.2%]. Postoperative radiotherapy was performed in 28.4% of patients because of positive surgical margin and in 22.2% due to inappropriate location of the tumor after bronchoscopic ablation. During a three-year follow up, one patient [11.1%] had tumor recurrence. Resection with post-operative radiotherapy was performed for him. The three-year survival was 88.8%. Because of the nature of adenoid cystic carcinoma of the trachea, surgical resection is the best method of treatment. But if surgical margins are positive post-operative radiotherapy will be necessary. In patients who are not candidates for resection, radiotherapy can be an effective alternative treatment

High dose-rate brachytherapy as a treatment option in primary tracheal tumors

OBJETIVO: Apresentar a experiência do tratamento de 4 pacientes com tumores primários de traquéia, não operados, submetidos à braquiterapia endobrônquica de alta taxa de dose. PACIENTES E MÉTODOS: Dois casos de carcinoma espinocelular, uma recidiva de carcinoma adenóide cístico e uma recidiva de plasmocitoma primário da traquéia. Todos receberam braquiterapia endobrônquica, exclusiva ou como reforço de dose da radioterapia externa. Foram administradas 3 ou 4 frações de 7,5 Gy cada, calculados a 1 cm de profundidade. O seguimento foi considerado a partir do término da braquiterapia. RESULTADOS: Em todos os casos houve resposta completa. Dois pacientes com carcinoma espinocelular evoluíram a óbito em 6 e 33 meses após a braquiterapia, o primeiro, sem evidência de doença e o outro por recidiva local, respectivamente. As outras 2 pacientes encontravam-se vivas após 64 e 110 meses de seguimento, sem evidência de doença. Esses 2 casos apresentaram estenose traqueal em 22 e 69 meses após a braquiterapia, sendo necessária a colocação de prótese traqueal apenas na paciente com carcinoma adenóide cístico. CONCLUSÕES: A braquiterapia endobrônquica de alta taxa de dose pode ser utilizada tanto como reforço de dose da irradiação externa quanto em recidivas. O controle local obtido em 3 de 4 pacientes indica que casos individuais podem se beneficiar desse procedimento. Sobrevida a longo prazo pode ser observada, principalmente nos casos de histologia adenóide cística.

Nd: YAG laser bronchoscopy; the first two successful cases in Puerto Rico

Two patients underwent bronchoscopic laser photoresection of tumors in the tracheobronchial tree with no mortality or significant morbidity. One patient had an adenoid cystic carcinoma of the trachea and the other a pleomorphic adenoma of left main stem bronchus. These were the first two cases performerd in Puerto Rico at San Pablo Medical Center. Both patients are symptomless at this time. We can conclude that laser is a safe and cost effective altenative in experienced hands to other procedures in properly selected patients with tumors of tracheobronchial tree in Puerto Rico