RESUMO
Abstract Type II Aortopulmonary window (APW) accounts for only 10% of total cases of APW, which by itself is a rare congenital anomaly. Various cardiac malformations have been reported to be associated with this rare anomaly. We report one such association of origin of left subclavian artery (LSCA) from left pulmonary artery (LPA) via ductus arteriosus that was surgically repaired.
Assuntos
Humanos , Defeito do Septo Aortopulmonar/cirurgia , Defeito do Septo Aortopulmonar/complicações , Defeito do Septo Aortopulmonar/diagnóstico por imagem , Artéria Subclávia/cirurgia , Artéria Subclávia/diagnóstico por imagem , Aorta Torácica/cirurgia , Aorta Torácica/diagnóstico por imagem , Artéria Pulmonar/cirurgia , Artéria Pulmonar/diagnóstico por imagem , PulmãoRESUMO
Abstract Aortopulmonary septal defect, also known as the aortopulmonary window, is a rare congenital macrovascular malformation. This case involves a 9-year-old boy with aortopulmonary septal defect (type I combined with type IV). Before surgery, milrinone and alprostadil were used to counteract high lung pressure. Surgery was performed under cardiopulmonary bypass, following which the pulmonary pressure decreased. The aorta was cut, and the right pulmonary artery opening was connected with the main pulmonary artery septal defect using polyester patch. An internal tunnel was made, and the deformity correction was completed. The child exhibited normal postoperative recovery with no discomfort. A complex aortopulmonary window is a rare condition that can be treated successfully with appropriate preoperative and surgical management.
Assuntos
Humanos , Masculino , Criança , Defeito do Septo Aortopulmonar/cirurgia , Aorta/cirurgia , Aorta/diagnóstico por imagem , Defeito do Septo Aortopulmonar/fisiopatologia , Defeito do Septo Aortopulmonar/diagnóstico por imagem , Artéria Pulmonar/cirurgia , Artéria Pulmonar/diagnóstico por imagem , Pressão Sanguínea , Ecocardiografia , Tomografia Computadorizada por Raios X , Resultado do Tratamento , Doenças RarasRESUMO
La ventana aortopulmonar es una causa poco frecuente de insuficiencia cardiaca en el neonato. Debe ser descartada en caso de existir edema pulmonar sin los shunts izquierda-derecha más frecuentes. Presentamos las imágenes ecocardiográficas de un recién nacido que ingresó con clínica de insuficiencia cardiaca en nuestra institución.
The aortopulmonary window is a rare cause of heart failure in the neonate. It must be ruled out if there are signs of pulmonary edema without the most frequents left-right shunts. We report the echocardiographic images of a newborn who was admitted with symptoms of heart failure at our institution.