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Indian J Hum Genet ; 2013 Oct-Dec ;19 (4): 491-493
Artigo em Inglês | IMSEAR | ID: sea-156622

RESUMO

A rare congenital defect in fusion of the anterior chest wall resulting in an extrathoracic location of the heart. Cantrell’s pentalogy is a congenital anomaly resulting from embryologic development defect and consists of the following: A deficiency of the anterior diaphragm, a midline supraumbilical abdominal wall defect, a defect in the diaphragmatic pericardium, congenital intracardiac abnormalities, and a defect of the lower sternum. Here


Assuntos
Adulto , Ectopia Cordis/epidemiologia , Ectopia Cordis/genética , Feminino , Hérnia Umbilical/epidemiologia , Hérnia Umbilical/genética , Hérnia Umbilical/mortalidade , Humanos , Recém-Nascido , Recém-Nascido Prematuro , Masculino , Natimorto
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