Assuntos
Humanos , Feminino , Adulto , Estenose Subvalvar Pulmonar/complicações , Ecocardiografia/métodos , Endocardite/complicações , Ecocardiografia Doppler/métodos , Ultrassonografia/métodos , Hipertrofia Ventricular Direita , Átrios do Coração , Cardiopatias Congênitas/complicações , Cardiopatias Congênitas/diagnóstico , Comunicação Interatrial , Ventrículos do CoraçãoRESUMO
Aneurysm of the main pulmonary artery is rare. Its natural history is not well understood and there are no clear guidelines regarding its optimal treatment. We present a case of a huge saccular aneurysm of the main pulmonary artery which was associated with infundibular and valvular pulmonary stenosis. It was repaired using a pericardial patch with concomitant pulmonary valvotomy and infundibular resection. Postoperative recovery was uneventful and the patient is doing well. Follow-up echocardiogram revealed good repair.
Assuntos
Aneurisma/complicações , Procedimentos Cirúrgicos Cardiovasculares , Humanos , Masculino , Pessoa de Meia-Idade , Artéria Pulmonar/patologia , Estenose Subvalvar Pulmonar/complicações , Obstrução do Fluxo Ventricular Externo/complicaçõesRESUMO
The cardiac manifestation usually associated with tuberous sclerosis is rhabdomyoma of the heart. We report a rare association with cyanotic congenital heart disease in the form of double outlet right ventricle with infundibular pulmonary stenosis.
Assuntos
Criança , Dupla Via de Saída do Ventrículo Direito/complicações , Feminino , Humanos , Estenose Subvalvar Pulmonar/complicações , Esclerose Tuberosa/complicaçõesRESUMO
Fifty one angiographically proved cases of tetralogy of Fallot (TOF) in the age group of 5-50 years were analysed retrospectively for the level(s) of right ventricular outflow tract (RVOT) obstruction. Mean age was 18.1 +/- 11 yrs. Subvalvular stenosis was found to be the commonest site of RVOT obstruction in 49 (96.1%) patients. Evidence of valvular pulmonary stenosis was seen quite commonly (42/51, 83.9% cases), mostly in association with obstruction at other sites. Supravalvular stenosis was also seen in 17 (33.3%) cases. Higher incidence of pulmonary valvular involvement in patients with TOF, in higher average age of patient population may represent valvular involvement to be an acquired phenomenon.