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2.
Rev. chil. cir ; 60(6): 557-560, dic. 2008. ilus
Artigo em Espanhol | LILACS | ID: lil-512409

RESUMO

El Tumor Desmolde o Fibromatosis Mesentérica es una enfermedad infrecuente en la que se reconocen 2 formas: una esporádica y otra asociada a poliposis familiar adenomatosa. De etiología desconocida, su diagnóstico preoperatorio es dificultoso y el tratamiento de elección es quirúrgico. Se pone en consideración un caso de esta entidad en un varón joven, que se presentó con dolor abdominal y fiebre. Se realizó cirugía resectiva agresiva, otorgándose el alta a los 18 días de la intervención.


Desmoid tumor or mesenteric fibromatosis is an uncommon disease with to variants: a sporadic form and one associated to familial adenomatous polyposis. Surgery is the treatment of choice. We report a 45 years old male presenting with abdominal pain and fever. An abdominal ultrasound informed the presence of a mass in the periumblical area. An Abdominal CAT sean showed a 13 cm diameter solid mass located in the left upper quadrant. The patient was operated and that mass is excised, requiring also a hemicolectomy, excision of the fourth portion of the duodenum and cholecystectomy. The pathology report of the excised tumor informs a mesenteric fibromatosis. The patient was discharged at the 18th postoperative day.


Assuntos
Humanos , Masculino , Pessoa de Meia-Idade , Fibromatose Abdominal/cirurgia , Fibromatose Abdominal/complicações , Mesentério , Neoplasias Peritoneais/cirurgia , Dor Abdominal/etiologia , Fibroma , Resultado do Tratamento
3.
Artigo em Inglês | IMSEAR | ID: sea-124858

RESUMO

Primary mesenteric fibromatosis is a rare condition. The aggressive nature of these tumors and the potential for major morbidity secondary to resection makes it a challenging disease for the surgeon. We report a case of mesenteric fibromatosis with involvement of small bowel.


Assuntos
Adulto , Duodenopatias/etiologia , Fibromatose Abdominal/complicações , Humanos , Fístula Intestinal/etiologia , Masculino , Mesentério , Neoplasias Peritoneais/complicações , Tomografia Computadorizada por Raios X
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