Himen imperforado con hematocolpos. A propósito de un caso / Imperforate hymen with hematocolpos. Apropos of a case

RESUMEN Los defectos en la canalización de la membrana himeneal causan obstrucción del tracto genital femenino. Como consecuencia aparece hematocolpos, resultante de la acumulación y retención de secreciones cervicovaginales -sangre en útero y vagina-, ante la imposibilidad de su evacuación por la presencia de un himen imperforado. Clínicamente aparece masa abdominal, asociada con malformaciones vaginales congénitas. Se presentó el caso de una adolescente de 13 años que refirió retención urinaria, disuria, dolor y masa en hipogastrio, y ausencia de la menarquía a pesar de un desarrollo puberal en estadio Tanner III. Al realizar ultrasonido se constató sangre en el útero, debido a imperforación himeneal que se resolvió mediante himenotomía. La patología de himen imperforado con hematocolpos debe estar entre los posibles planteamientos sindrómicos de aquellas pacientes con cuadros similares; puede diagnosticarse en la Atención Primaria de Salud a partir de una detallada anamnesis y exploración física, aunque la comprobación requiere ecografía (AU).

ABSTRACT The defects in the channeling of the himeneal membrane cause obstruction in the female genital tract. As consequence hematocolpos appears, resulting from the accumulation and retention of cervicovaginal secretions -blood in the uterus and vagina-, due to the impossibility of its evacuation because of the presence of an imperforate hymen. Clinically, abdominal mass appears associated to congenital vaginal malformations. We presented the case of teenager aged 13 years that referred urine retention, dysuria, pain, had a mass in the hypogastrium, and absence of menarche in spite of a Tanner III pubertal development. An ultrasound showed blood in the uterus due to hymeneal imperforation solved through hymenotomy. The pathology of imperforate hymen with hematocolpos should be among the possible syndrome considerations in those patients with the same characteristics; it can be diagnosed in the primary health care from anamnesis and physical exploration, although the verification requires an ultrasound (AU).

Síndrome de Herlyn-Werner-Wunderlich. Síndrome OHVIRA. Reporte de Caso / Herlyn-Werner-Wunderlich Syndrome or OHVIRA Syndrome. Case Report

Paciente Femenina de 11 años con el síndrome de Herlyn-Werner-Wunderlich, manejado multdisciplinariamente y resuelto endoscópicamente con una septotomía y dilataciones vaginales.

This case is about a female patent, 11 years old, with Herlyn-Werner-Wunderlich Syndrome, who received multdisciplinary approach and was endoscopically resolved with septotomy and vaginal dilatatons.

Uterine didelphus with obstructed hemivagina

Complex congenital anomalies of the mullerian ducts can occur in isolation or in association with other developmental disorders. They result from non-development or non-fusion of the mullerian ducts or the failure of reabsorption of the uterine septum. Early diagnosis is necessary to relieve symptoms, optimize preservation of the genital organs and prevent the development of endometriosis. We present a case report to highlight this phenomenon

Didelphys uterus associated with haematocolpos and ipsilateral renal agenesis presented as acute abdomen

Malformation of the female genital tract can be associated with various urinary tract anomalies, but double uterus with partially or completely obstructed vagina, and ipsilateral renal aplasia is quite rare. The clinical presentation varies, depending on the utero- vaginal relationship which may obscure the true diagnosis. Because menses in patients with this syndrome are rarely regular, the physician can easily overlook the possibility of this diagnosis. We describe a case of didelphys uterus associated with haematocolpos and ipsilateral renal agenesis presented as acute abdomen

Acute urinary retention associated with unilateral hematocolpos and ipsilateral renal agenesis

A virgin girl presented with acute urinary retention due to uterus bicornis associated with unilateral hematocolpos and ipsilateral renal agenesis. This is the third case to be reported in the literature. The management, which can be very challenging in societies which consider virginity essential in girls, is briefly discussed

Congenital hematometrocolpos in a circumcised girl. an anomaly superimposed by cultural mutilating practices

A rare case associated with congenital hematometrocolpos in a circumcised 13 years old Somalian girl is presented. Emphasis on proper history is highlighted. Mutilation caused by bad cultural practice of female circumcision which is although not a problem in Pakistan, is brought into notice for those who may be unaware of perineal appearance of a circumcised female and stitched over vagina

Himen imperforado / Imperforate hymen

Se presenta un caso clínico de himen imperforado. Se describe el rol de la ecografía en su manejo y las alternativas terapéuticas actuales

Diagnóstico ecográfico de hidro ou hematométrio associado ou näo a hidro ou hematocolpus: apresentaçäo de 5 casos / Ecographic diagnosis of hydro or hematometra associated or not to hydro or hematocolpos: report of 5 cases

Relatam-se 5 casos de hematométrio e hematocolpus. Discutem-se os resultados ecográficos característicos dessas afecçöes que säo mais freqüentes em grupos mais jovens e em idosos. Recomendam-se incorporar o ultra-som pélvico na pesquisa clínica dessas pacientes e estender o exame a outros órgäos, especialmente o sistema renal infantil