Uso del sildenafilo oral en el tratamiento del linfangioma orbitario / Use of Oral Sildenafil in the Treatment of Orbital Lymphangioma

Los linfangiomas orbitarios son malformaciones vasculares benignas, de crecimiento lento, abortivas y no funcionales, que se presentan principalmente en la primera década de la vida. Las opciones terapéuticas en estos casos presentan una resolutividad limitada, algunos tratamientos suelen ser agresivos y provocar daños del aparato visual. Se presenta un caso de una paciente femenina de 6 años de edad atendida por proptosis del ojo izquierdo a la que se le realizó el diagnóstico clínico-imagenológico de linfangioma de la órbita, con el objetivo de mostrar el resultado alcanzado en el manejo de la misma mediante el uso del sildenafilo por vía oral, modalidad terapéutica en estudio a nivel mundial en el tratamiento de estas afecciones. El tratamiento con sildenafilo en el linfangioma orbitario demostró ser eficaz en la mejoría del cuadro clínico y por imágenes. Durante el tratamiento no se reportaron reacciones adversas(AU)

Orbital lymphatic malformations are benign, slow-growing, abortive, nonfunctional vascular malformations that occur mainly in the first decade of life. Therapeutic options in these cases present limited resolution, some treatments are usually aggressive and cause damage to the visual apparatus. We present a case of a 6-year-old female patient treated for proptosis of the left eye. The clinical-imaging diagnosis of lymphangioma of the orbit was made to show the results achieved in its treatment through the use of oral sildenafil, a therapeutic modality under study worldwide in the treatment of these conditions. The treatment with sildenafil in orbital lymphangioma proved to be effective in the improvement of the clinical and imaging picture. No adverse reactions were reported during treatment(AU)

Lymphangioma secondary to irradiation after mastectomy

Abstract Lymphangioma is a rare benign disease of the lymphatic vessels. Typically, they are primary conditions but may be acquired secondarily, such as those caused by irradiation during radiotherapy for the treatment of breast cancer. The local lymphatic obstruction provoked by irradiation causes the appearance of asymptomatic hyaline vesicles on the irradiated skin. The present report describes a 78-year-old female patient, who initially presented hyaline vesicles that progressed into multiple papules with serous exudation of a yellowish and odorless secretion on the area of chronic radiodermitis in right breast. Despite the rarity of the case, we emphasize the importance of knowledge regarding dermatological disease for early diagnosis and proper medical conduct.

Linfangioma circunscrito adquirido: a propósito de un caso / Acquired lymphangioma circumscriptum: a case report

Los linfagiomas adquiridos son dilataciones de los vasos linfáticos que pueden resultar como complicación de cirugía o radioterapia. Comparten características clínicas e histológicas con aquellos de las lesiones congénitas. El diagnóstico y tratamiento de estas lesiones vesiculobulosas son importantes, ya que se pueden asociar con dolor y celulitis. Presentamos el caso de una paciente que presentó estas lesiones tras tratamiento de un cáncer de mama.

Acquired lymphangiomas are dilatations of lymphatic vessels that can result as a complication of surgical or radiation therapy. They share clinical and histological features with those of congenital lesions. Diagnosis and treatment of this vesiculobullous lesion are important because it may be associated with pain and cellulitis. We describe a patient who presented these lesions after treatment of mammary cancer.

Tumores neonatales bucomaxilofaciales / Neonatal buccomaxillofacial tumors

Se realiza un estudio descriptivo, lineal y retrospectivo por un período de 10 años, de 11 recién nacidos (edad 0-30 días), quienes al nacer presentan en la región bucomaxilofacial un tumor que les ocasiona de manera determinante compromiso para la ventilación y/o alimentación, por lo que se hace necesario realizarles a todos de manera inmediata, tratamiento quirúrgico para preservarles la vida. Se analizaron las variables edad, sexo, color de la piel, diagnóstico, tumoraciones que se presentaron con mayor frecuencia, compromiso para la ventilación y/o alimentación, procederes y mortalidad. Los datos se recogieron en una planilla confeccionada al efecto, lo que permitió establecer resultados y confeccionar tablas. Se concluye que en nuestro estudio este tipo de tumoración afectó con mayor frecuencia al sexo femenino y a niños de piel blanca; y el tipo de tumoración observada con mayor frecuencia fueron las malformaciones vasculares de tipo linfático (linfangiomas gigantes o higromas quísticos), así como y los teratomas bucofaríngeos, con una mortalidad de alrededor del 27,3 por ciento en estas edades neonatales(AU)

A descriptive, lineal and retrospective study of 11 newborn infants aged 0-30 days was conducted. They presented a tumor in the buccomaxillofacial region that compromised their ventilation and/or nutrition, which made necessary to immediately perform surgery to preserve their lives. The following variables were analyzed: age, sex, colour of the skin, diagnosis, the most common tumours, compromise for ventilation and/or nutrition, procedures and mortality. Data were collected in a form that allowed to establish results and to make tables. It was concluded that this type of tumor affected mostly females and white children. The most commonly observed tumors were vascular lymphatic malformations (giant lymphangiomas or cystic hygromas), as well as buccopharyngeal teratomas, with a mortality around 27,3 percent at these neonatal ages(AU)

Linfangioma cístico do pâncreas: relato de caso / Cystic lymphangioma of the pancreas: case report

Linfangiomas são tumores benignos incomuns. Geralmente têm sido descritos em regiões como cabeça, pescoço e axila. Linfangiomas pancreáticos acometem predominantemente indiv¡duos do sexo feminino, são extremamente raros e correspondem a apenas 1% de todos os linfangiomas. Esses tumores geralmente causam sintomas como dor abdominal ou vômitos. O diagnóstico radiológico e o tratamento, a ressecção cirúrgica. Os autores relatam um caso de linfangioma cístico do pâncreas, em uma paciente do sexo feminino de 70 anos, com quadro clínico de dor abdominal, que foi submetida … pancreatectomia central com sucesso.

The fate of traumatic subdural hygroma in serial computed tomographic scans

We reviewed serial computed tomographic (CT) scans of 58 patients with traumatic subdural hygroma (SDG) to investigate its natural history. All were re-evaluated with a special reference to the size and density of SDG. Thirty-four patients (58.6%) were managed conservatively and 24 patients (41.4%) underwent surgery. The lesion was described as remained, reduced, resolved, enlarged and changed. Means of interval from injury to diagnosis and any changes in CT were calculated. SDGs were resolved in 12 (20.7%), reduced in 15 (25.9%), remained in 10 (17.2%), enlarged in 2 (3.4%), and changed into chronic subdural hematoma (CSDH) in 19 patients (32.8%). SDG was diagnosed at 11.6 days after the injury. It was enlarged at 25.5 days, remained at 46.0 days, reduced at 59.3 days, resolved at 107.5 days, and changed into CSDH at 101.5 days in average. SDGs were developed as delayed lesions, and changed sequentially. They enlarged for a while, then reduced in size. The final path of a SDG was either resolution or CSDH formation. Nearly half of SDGs was resolved or reduced within three months, however, 61.3% of unresolved or unreduced SDG became iso- or hyperdense CSDH. These results suggest that the unresolved SDG is the precursor of CSDH.

Linfangiomas abdominales: breve revisión / Abdominal linfangiomas: brief review

El linfangioma abdominal es una entidad rara y poco conocida en pediatría. Consiste en una alteración congénita del desarrollo de los vasos linfáticos con formación de quistes de diferente tamaño al interior del abdomen. Se originaría por el aislamiento de sacos linfáticos primitivos del resto del sistema linfático y venoso. Sus manifestaciones clínicas fluctúan desde un abdomen agudo, hasta un paciente asintomático, pasando por la obstrucción intestinal parcial, y la palpación casual de una masa abdominal. Los estudios de imágenes de elección son la ultrasonografía y la tomografía axial computarizada; permiten visualizar la conformación del quiste, así como sus relaciones con los órganos vecinos. El tratamiento es siempre quirúrgico, y consiste en la extirpación total o parcial de los quistes. No se ha descrito malignización, por lo que el pronóstico es generalmente bueno

Submucosal lymphatic cyst of the stomach

A submucosal lymphatic cyst is a thin-walled cyst, lined by flattened lymphatic endothelium, containing thin serous fluid. It rarely causes clinical symptoms, and it is incidentally discovered during fiberoptic panendoscopy or radiologic study in most cases. It is an extremely rare benign tumor of the stomach; however, a submucosal lymphatic cyst should be considered if a pliable and benign submucosal lesion is detected during fiberoptic panendoscopy. We report a case of submucosal lymphatic cyst of the stomach which showed a typical clinical picture. This report is the first case of submucosal lymphatic cyst of the stomach in Korea to the best of our knowledge.

Submucosal lymphatic cyst of the stomach

A submucosal lymphatic cyst is a thin-walled cyst, lined by flattened lymphatic endothelium, containing thin serous fluid. It rarely causes clinical symptoms, and it is incidentally discovered during fiberoptic panendoscopy or radiologic study in most cases. It is an extremely rare benign tumor of the stomach; however, a submucosal lymphatic cyst should be considered if a pliable and benign submucosal lesion is detected during fiberoptic panendoscopy. We report a case of submucosal lymphatic cyst of the stomach which showed a typical clinical picture. This report is the first case of submucosal lymphatic cyst of the stomach in Korea to the best of our knowledge.