Assuntos
Humanos , Masculino , Pré-Escolar , Colesteatoma da Orelha Média/diagnóstico por imagem , Neoplasias Primárias Múltiplas/diagnóstico por imagem , Colesteatoma da Orelha Média/cirurgia , Colesteatoma da Orelha Média/congênito , Tomografia Computadorizada Multidetectores , Neoplasias Primárias Múltiplas/cirurgia , Neoplasias Primárias Múltiplas/congênitoRESUMO
Three cases of extragonadal teratomas presented at birth and all the cases arisen from three separate sites are reported in the present study. A huge sacrococcygeal teratoma is being reported and the other two retroperitoneal and nasopharyngeal teratomas, are reported for the rarity of their location in neonatal period. Teratomas of all three babies were mature benign on histopathology and surgical removal sufficed as mode of treatment. No recurrence was noted on follow-up.
Assuntos
Feminino , Virilha/patologia , Humanos , Recém-Nascido , Masculino , Neoplasias Primárias Múltiplas/congênito , Neoplasias Faríngeas/congênito , Faringe/patologia , Neoplasias Retroperitoneais/congênito , Região Sacrococcígea/patologia , Neoplasias da Coluna Vertebral/congênito , Teratoma/congênitoRESUMO
Congenital plexiform neurofibroma is regarded as pathognomonic of neurofibromatosis (NF) especially when it is large and involves a major nerve trunk with changes of elephantiasis neuromatosa. Only very rarely malignant changes have been reported in cases who have NF for less than 5 years. 'Borderline' lesions are seen especially in patients with NF. In such cases criteria of mitotic activity should be utilized in establishing the diagnosis of malignancy. A case of 3 month child with congenital plexiform neurofibroma involving neck with elephantiasis neuromatosa with sarcomatous nodule has been described in the present article. The criteria for malignancy in nerve sheath tumors have also been discussed.