RESUMO
Introduction: Contrary to its name, synovial sarcoma does not arise from the synovial membrane but from multi-potent stem cells and can present in any part of the body. Very few cases of vulval synovial sarcoma have been reported in the literature; we report on such a presentation. Th ese tumors can present as painless lumps, which must be completely excised to give the best prognosis. Th erefore the diagnosis of synovial sarcoma should always be kept in mind in the management of vulval masses, especially in young patients.
Assuntos
Adulto , Povo Asiático , Feminino , Humanos , Células-Tronco Multipotentes/diagnóstico , Células-Tronco Multipotentes/terapia , Prognóstico , Sarcoma Sinovial/diagnóstico , Sarcoma Sinovial/epidemiologia , Sarcoma Sinovial/radioterapia , Vulva/patologia , Vulva/terapiaRESUMO
Synovial sarcomas are most frequently observed in the extremities. A lthough synovial sarcomas are the third most common histological type of soft-tissue sarcomas of the extremities, primary mediastinal synovial sarcoma is extremely rare. Monophasic synovial sarcoma is the most commonly observed subtype. whereas the biphasic subtype is less common. We present our case which was diagnosed as biphasic synovial sarcoma located in the anterior mediastinum, which is considered to be a rare entity. The patient underwent surgical resection together with multimodal adjuvant radiotherapy and chemotherapy