RESUMO
Myelodysplastic syndrome (MDS) is a heterogenous group of stem cell disorders usually characterized by progressive refractory cytopenias, which could progress to acute myeloid leukemia. MDS may be associated with a wide spectrum of skin lesions, including neoplastic cell infiltration, Sweet's syndrome, pyoderma gangrenosum, erythema elevatum diutinum, vasculitis, and panniculitis. However, erythema nodosum is rarely associated with MDS. Unusual rheumatologic manifestations in patients with MDS also have been reported, which range from asymptomatic serological abnormalities to classic connective tissue disorders such as Sjogren's syndrome, relapsing polychondritis, systemic lupus erythematosus, rheumatoid arthritis and mixed connective tissue disease. However, concurrent erythema nodosum and serositis has rarely been reported. We describe a case of MDS with erythema nodosum and immune-mediated pericardial effusion in a 34-year-old woman.
Assuntos
Adulto , Feminino , Humanos , Biópsia , Diagnóstico Diferencial , Eritema Nodoso/complicações , Seguimentos , Glucocorticoides/uso terapêutico , Síndromes Mielodisplásicas/complicações , Prednisona/uso terapêutico , Serosite/complicações , Tomografia Computadorizada por Raios XAssuntos
Humanos , Feminino , Pessoa de Meia-Idade , Leucemia Mielomonocítica Crônica/patologia , Xantomatose/patologia , Artrite/complicações , Eritema Nodoso/complicações , Evolução Fatal , Leucemia Mielomonocítica Crônica/complicações , Serosite/complicações , Vasculite/complicações , Xantomatose/complicaçõesRESUMO
Two patients with extensive spontaneous venous thrombosis are reported. Both had documented evidence of polyserositis, transient abnormalities of liver function tests along with normal coagulograms. Although one patient had a short, self-limiting illness, the other required treatment with coumarin derivatives. The relevant literature is discussed.