A case of Kartagener’s syndrome: Importance of early diagnosis and treatment.

Kartagener’s syndrome is a very rare congenital malformation comprising of a classic triad of sinusitis, situs inversus and bronchiectasis. Primary ciliary dyskinesia is a genetic disorder with manifestations present from early life and this distinguishes it from acquired mucociliary disorders. Approximately one half of patients with primary ciliary dyskinesia have situs inversus and, thus are having Kartagener syndrome. We present a case of 12 year old boy with sinusitis, situs inversus and bronchiectasis. The correct diagnosis of this rare congenital autosomal recessive disorder in early life is important in the overall prognosis of the syndrome, as many of the complications can be prevented if timely management is instituted, as was done in this in this case.

Dextrocardia em situs inversus totalis com doença obstrutiva coronária: tratamento pela angioplastia coronária por via braquial / Dextrocardia with coronary disease in situs inversus totalis. treatment with coronary angioplasty by brachial approach

A dextrocardia em "situs inversus totalis" com lesão obstrutiva coronária é uma situação rara, existindo na literatura referência a apenas alguns casos tratados pela angioplastia coronária por via femoral. No presente trabalho descreve-se o caso de um paciente de 61 anos submetido com sucesso à dilatação de duas artérias por via braquial. Discutem-se aspectos técnicos relacionados com o procedimento, o qual pode ser facilmente executado, desde que se disponha de material adequado

Dextrocardia in "situs inversus totalis" with obstructive coronary disease is a rare clinical situation, with few cases treated by coronary angioplasty using the femoral approach being reported. In this report we describe the case of a 61-year-old male patient who underwent successful! dilatation of two arteries by the brachial approach. We discuss technical aspects related to the procedure, which may be easily performed when proper equipment is available