Eosinophilic granulomatosis with polyangiitis: a challenge for differential diagnosis / Granulomatosis eosinofílica con poliangitis: un desafío para el diagnóstico diferencial
Salud UNINORTE
;
34(2): 527-530, mayo-ago. 2018.
Article
in English
|
LILACS-Express
| LILACS
| ID: biblio-1004602
ABSTRACT
Abstract Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a rare small and medium vessels vasculitis, consisting of asthma, migratory pulmonary infiltrates and eosinophilia. Its low occurrence makes it difficult to achieve an early diagnosis, and hence a directed treatment in order to control it and avoid complications. We report a 31 year-old man with refractory asthma, who developed arthritis and multiplex mononeuritis. Before EGPA's diagnosis, he had just received asthma treatment (steroids, bronchodilators, antileukotriene and omalizumab); but once EGPA is confirmed and correct treatment was started, there was a remarkable clinical improvement.
RESUMEN
Resumen La granulomatosis eosinofílica con poliangitis (EGPA), anteriormente conocida como síndrome de Churg-Strauss, es una vasculitis poco frecuente de vasos pequeños y medianos, que consiste en asma, infiltrados pulmonares migratorios y eosinofilia. Su baja aparición dificulta el diagnóstico precoz y, por lo tanto, un tratamiento dirigido para controlarlo y evitar complicaciones. Presentamos a un hombre de 31 años con asma refractaria, que desarrolló artritis y mononeuritis múltiple. Antes del diagnóstico de EGPA, acababa de recibir tratamiento para el asma (esteroides, broncodilatadores, antileucotrienos y omalizumab); pero una vez que se confirmó la EGPA y se inició el tratamiento correcto, hubo una mejoría clínica notable.
Full text:
Available
Index:
LILACS (Americas)
Type of study:
Diagnostic study
/
Screening study
Language:
English
Journal:
Salud UNINORTE
Journal subject:
Public Health
Year:
2018
Type:
Article
Affiliation country:
Colombia
Institution/Affiliation country:
Universidad del Norte/CO
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