Neurofibrosarcoma of the mandible derived from neurofibromatosis
Autops. Case Rep
;
9(4): e2019094, Oct.-Dec. 2019. ilus
Article
in English
| LILACS
| ID: biblio-1024293
ABSTRACT
Neurofibrosarcoma is a rare malignant neoplasm of the head and neck region and accounts for 8% to 16% of all cases. Its origin is varied and may stem from cells of the peripheral nerves, develop de novo, or result from malignant transformation of preexisting neurofibromas. Because the features of neurofibrosarcomas are heterogeneous, the data retrieved during clinical examinations are of great aid for diagnosis. In this case, owing to clinical features and the fact that the patient had neurofibromatosis type 1, the hypothesis of neurofibrosarcoma was promptly established. The final diagnosis was confirmed by associating clinical, imaging, and pathological data. After the treatment, the patient has been followed up for 10 years, with no evidence of recurrence.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Mouth Neoplasms
/
Neurofibromatosis 1
/
Neurofibrosarcoma
Limits:
Adolescent
/
Female
/
Humans
Language:
English
Journal:
Autops. Case Rep
Journal subject:
Anatomia
/
Patologia Cl¡nica
/
Patologia Legal
Year:
2019
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Hospital Heliopolis/BR
/
Universidade de São Paulo/BR
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