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Lupus eritematoso sistémico asociado a síndrome de McCune-Albright: reporte de un caso / Systemic lupus erythematosus associated a McCune-Albright syndrome: case report
Acosta, J. M; Herrera, C. N.
  • Acosta, J. M; Hospital Roberto Gilbert Elizalde. Guayaquil. EC
  • Herrera, C. N; Hospital Roberto Gilbert Elizalde. Guayaquil. EC
Rev. argent. endocrinol. metab ; 55(3): 51-60, set. 2018. graf
Article in Spanish | LILACS | ID: biblio-1041744
RESUMEN
RESUMEN El Síndrome de McCune-Albright (SMA) es una enfermedad poco frecuente compuesta por una tríada clásica displasia fibrosa poliostótica (DFP), manchas cutáneas de color café con leche y alteraciones endocrinas, siendo la más frecuente la pubertad precoz. Este síndrome no se ha visto asociado a enfermedades autoinmunes. Reportamos el primer caso de una paciente con SMA y lupus eritematoso sistémico.
ABSTRACT
ABSTRACT McCune-Albright Syndrome (MAS) is a rare disease characterized by a classical triad polyostotic fibrous dysplasia (PFD), cafe-au-lait macules and endocrine abnormalities, most frequently precocious puberty. This syndrome has not been associated with autoimmune diseases. We report the first case of a patient with MAS and systemic lupus erythematosus.
Subject(s)

Full text: Available Index: LILACS (Americas) Main subject: Fibrous Dysplasia, Polyostotic / Lupus Erythematosus, Systemic Type of study: Diagnostic study / Risk factors Limits: Child / Female / Humans Language: Spanish Journal: Rev. argent. endocrinol. metab Journal subject: Endocrinology / Metabolism Year: 2018 Type: Article Affiliation country: Ecuador Institution/Affiliation country: Hospital Roberto Gilbert Elizalde/EC

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Full text: Available Index: LILACS (Americas) Main subject: Fibrous Dysplasia, Polyostotic / Lupus Erythematosus, Systemic Type of study: Diagnostic study / Risk factors Limits: Child / Female / Humans Language: Spanish Journal: Rev. argent. endocrinol. metab Journal subject: Endocrinology / Metabolism Year: 2018 Type: Article Affiliation country: Ecuador Institution/Affiliation country: Hospital Roberto Gilbert Elizalde/EC