Lupus eritematoso sistémico asociado a síndrome de McCune-Albright: reporte de un caso / Systemic lupus erythematosus associated a McCune-Albright syndrome: case report
Rev. argent. endocrinol. metab
;
55(3): 51-60, set. 2018. graf
Article
in Spanish
| LILACS
| ID: biblio-1041744
RESUMEN
RESUMEN El Síndrome de McCune-Albright (SMA) es una enfermedad poco frecuente compuesta por una tríada clásica displasia fibrosa poliostótica (DFP), manchas cutáneas de color café con leche y alteraciones endocrinas, siendo la más frecuente la pubertad precoz. Este síndrome no se ha visto asociado a enfermedades autoinmunes. Reportamos el primer caso de una paciente con SMA y lupus eritematoso sistémico.
ABSTRACT
ABSTRACT McCune-Albright Syndrome (MAS) is a rare disease characterized by a classical triad polyostotic fibrous dysplasia (PFD), cafe-au-lait macules and endocrine abnormalities, most frequently precocious puberty. This syndrome has not been associated with autoimmune diseases. We report the first case of a patient with MAS and systemic lupus erythematosus.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Fibrous Dysplasia, Polyostotic
/
Lupus Erythematosus, Systemic
Type of study:
Diagnostic study
/
Risk factors
Limits:
Child
/
Female
/
Humans
Language:
Spanish
Journal:
Rev. argent. endocrinol. metab
Journal subject:
Endocrinology
/
Metabolism
Year:
2018
Type:
Article
Affiliation country:
Ecuador
Institution/Affiliation country:
Hospital Roberto Gilbert Elizalde/EC
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