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Rare association between atrioventricular septal defect and partial anomalous pulmonary venous connection
Murakami, Alexandre Noboru; Baston, Gabriela Guimarães; Cardoso, Mariana Ribeiro Rodero; Marchi, Carlos Henrique De; Croti, Ulisses Alexandre.
  • Murakami, Alexandre Noboru; Universidade Estadual de Londrina (UEL). Serviço de Cirurgia Cardíaca do Norte do Paraná. Londrina. BR
  • Baston, Gabriela Guimarães; Faculdade de Medicina de São José do Rio Preto (FAMERP). Hospital da Criança e Maternidade de São José do Rio Preto (FUNFARME). Pediatric Cardiovascular Surgery Department. BR
  • Cardoso, Mariana Ribeiro Rodero; Faculdade de Medicina de São José do Rio Preto (FAMERP). Hospital da Criança e Maternidade de São José do Rio Preto (FUNFARME). Pediatric Cardiovascular Surgery Department. BR
  • Marchi, Carlos Henrique De; Faculdade de Medicina de São José do Rio Preto (FAMERP). Hospital da Criança e Maternidade de São José do Rio Preto (FUNFARME). Pediatric Cardiovascular Surgery Department. BR
  • Croti, Ulisses Alexandre; Faculdade de Medicina de São José do Rio Preto (FAMERP). Hospital da Criança e Maternidade de São José do Rio Preto (FUNFARME). Pediatric Cardiovascular Surgery Department. BR
Rev. bras. cir. cardiovasc ; 34(6): 765-768, Nov.-Dec. 2019. tab, graf
Article in English | LILACS | ID: biblio-1057488
ABSTRACT
Abstract Clinical data Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation. Chest radiography Demonstrates cardiomegaly and prominent pulmonary vascular markings. Electrocardiography Shows right ventricular hypertrophy and left anterior fascicular block. Echocardiography Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein. Computed tomography angiography This complementary imaging exam was performed to confirm the diagnosis. Diagnosis The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated. Operation The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.
Subject(s)


Full text: Available Index: LILACS (Americas) Main subject: Abnormalities, Multiple / Vascular Malformations / Heart Defects, Congenital / Heart Septal Defects, Atrial Type of study: Risk factors Limits: Female / Humans / Infant Language: English Journal: Rev. bras. cir. cardiovasc Journal subject: Cardiology / General Surgery Year: 2019 Type: Article Affiliation country: Brazil Institution/Affiliation country: Faculdade de Medicina de São José do Rio Preto (FAMERP)/BR / Universidade Estadual de Londrina (UEL)/BR

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Full text: Available Index: LILACS (Americas) Main subject: Abnormalities, Multiple / Vascular Malformations / Heart Defects, Congenital / Heart Septal Defects, Atrial Type of study: Risk factors Limits: Female / Humans / Infant Language: English Journal: Rev. bras. cir. cardiovasc Journal subject: Cardiology / General Surgery Year: 2019 Type: Article Affiliation country: Brazil Institution/Affiliation country: Faculdade de Medicina de São José do Rio Preto (FAMERP)/BR / Universidade Estadual de Londrina (UEL)/BR