Familial "benign" pemphigus? Erythroderma and fatal outcome
An. bras. dermatol
;
95(1): 75-77, Jan.-Feb. 2020. graf
Article
in English
| LILACS
| ID: biblio-1088714
ABSTRACT
Abstract Hailey-Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey-Hailey disease with erythroderma and fatal outcome.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Pemphigus, Benign Familial
/
Dermatitis, Exfoliative
Limits:
Female
/
Humans
Language:
English
Journal:
An. bras. dermatol
Journal subject:
Dermatology
Year:
2020
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Santa Casa de Misericórdia de Porto Alegre/BR
/
Secretaria Estadual de Saúde/BR
/
Universidade Federal de Ciências da Saúde/BR
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