Esclerodermia y Cirrosis Biliar Primaria (Síndrome de Reynolds): Descripción de un Caso / Scleroderma and Primary Biliary Cirrhosis (Reynolds syndrome): Case Description
Rev. méd. Panamá
;
39(1): 25-27, 2019.
Article
in Spanish
| LILACS
| ID: biblio-1102342
RESUMEN
El síndrome de Reynolds, se define como cirrosis biliar primaria en pacientes con esclerodermia; este síndrome debe ser sospechado en aquellos pacientes que desarrollen un patrón colestásico. Se reporta una paciente con antecedente de esclerodermia que se presenta con ictericia, a quien se le confirma con estudios inmunológicos y biopsia hepática, el diagnóstico de cirrosis biliar prima ria (ahora se denomina colangitis biliar primaria). Se ordena ácido ursodesoxicólico 15mg/día.
ABSTRACT
Reynolds syndrome is defined as primary biliary cirrhosis in patients with scleroderma; this syndrome should be suspected in those patients who develop a cholesteric pattern. We report a patient with scleroderma who presented with jaundice. After immunological and liver biopsy, a diagnosis of Primary Biliary Cholangiopathy (new name) was confirmed. Ursodeoxycholic acid 15mg / day was prescribed
Full text:
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Index:
LILACS (Americas)
Main subject:
Scleroderma, Systemic
/
Liver Cirrhosis, Biliary
Limits:
Female
/
Humans
Language:
Spanish
Journal:
Rev. méd. Panamá
Journal subject:
Medicine
Year:
2019
Type:
Article
Affiliation country:
Colombia
Institution/Affiliation country:
Universidad Libre Seccional Barranquilla/CO
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