Caso clínico: agenesia pericárdica, diagnóstico imagenológico de una patología infrecuente / Clinical case: pericardial agenesis, radiological diagnosis of a rare disease
Rev. chil. radiol
;
26(2): 72-75, jun. 2020. graf
Article
in Spanish
| LILACS
| ID: biblio-1126196
RESUMEN
Resumen La agenesia pericárdica congénita es una condición infrecuente, que generalmente cursa de forma asintomática y es diagnosticada como hallazgo radiológico. Sin embargo, se describe la asociación con malformaciones cardiacas y herniaciones del miocardio con el subsiguiente riesgo de muerte súbita. La radiografía de tórax es un pilar fundamental para la sospecha diagnóstica. Presentamos un caso clínico de una paciente de 11 años que consulta por dolor torácico y disnea, que frente a los hallazgos típicos en radiografía de tórax se sospecha agenesia pericárdica, posteriormente confirmada con TC y RM.
ABSTRACT
Abstract Congenital pericardial agenesis is an infrequent but usually asymptomatic condition, and is diagnosed as an incidental radiological finding. However, the association with cardiac malformations and myocardial herniation with the subsequent risk of sudden death has been reported. Chest plain films are a fundamental tool to raise the diagnostic suspicion. We present a clinical case of an 11-year-old patient who consulted for chest pain and dyspnea, in which, with the typical findings on chest radiography, pericardial agenesis was suspected and later confirmed by CT and MRI.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Pericardium
/
Heart Defects, Congenital
Type of study:
Diagnostic study
Limits:
Child
/
Female
/
Humans
Language:
Spanish
Journal:
Rev. chil. radiol
Journal subject:
Radiology
Year:
2020
Type:
Article
Affiliation country:
Chile
Institution/Affiliation country:
Universidad del Desarrollo/CL
Similar
MEDLINE
...
LILACS
LIS