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A rare cecal subepithelial tumor in a Crohn´s Disease patient
Silva, Joana Inês Alves da; Caetano, Cidalina; Rocha, Anabela Maria Sousa da; Lamas, Nuno Jorge; Lago, Paula; Pedroto, Isabel Maria Teixeira de Carvalho.
  • Silva, Joana Inês Alves da; Centro Hospitalar Universitário do Porto. Department of Gastroenterology. Porto. PT
  • Caetano, Cidalina; Centro Hospitalar Universitário do Porto. Department of Gastroenterology. Porto. PT
  • Rocha, Anabela Maria Sousa da; Centro Hospitalar Universitário do Porto. General Surgery Service. Colorectal Unit. Porto. PT
  • Lamas, Nuno Jorge; Centro Hospitalar Universitário do Porto. Pathology Department. Anatomic Pathology Service. Porto. PT
  • Lago, Paula; Centro Hospitalar Universitário do Porto. Department of Gastroenterology. Porto. PT
  • Pedroto, Isabel Maria Teixeira de Carvalho; Centro Hospitalar Universitário do Porto. Department of Gastroenterology. Porto. PT
Autops. Case Rep ; 11: e2020211, 2021. tab, graf
Article in English | LILACS | ID: biblio-1142396
ABSTRACT
Appendiceal tumors comprise a variety of histologic types, including appendiceal mucinous neoplasms, which can be grouped as premalignant lesions, tumors of uncertain malignant potential, and malignant lesions. The appendiceal mucinous neoplasms are characterized by mucinous epithelial proliferation with extracellular mucin and pushing tumor margins, commonly an incidental finding during operative exploration. We report the case of a low-grade appendiceal mucinous neoplasm presenting as a subepithelial lesion in Crohn´s Disease patient. The diagnosis was not straightforward, and only surgical resection allowed an accurate diagnosis. Although Inflammatory Bowel Disease is a risk factor for the development of colorectal neoplasms, the absolute risk for appendiceal tumors is uncertain. The frequency of progression to malignancy remains to be determined.
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Full text: Available Index: LILACS (Americas) Main subject: Appendiceal Neoplasms / Colorectal Neoplasms / Neoplasms, Cystic, Mucinous, and Serous Type of study: Etiology study / Risk factors Limits: Female / Humans Language: English Journal: Autops. Case Rep Journal subject: Anatomia / Patologia Cl¡nica / Patologia Legal Year: 2021 Type: Article Affiliation country: Portugal Institution/Affiliation country: Centro Hospitalar Universitário do Porto/PT

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Full text: Available Index: LILACS (Americas) Main subject: Appendiceal Neoplasms / Colorectal Neoplasms / Neoplasms, Cystic, Mucinous, and Serous Type of study: Etiology study / Risk factors Limits: Female / Humans Language: English Journal: Autops. Case Rep Journal subject: Anatomia / Patologia Cl¡nica / Patologia Legal Year: 2021 Type: Article Affiliation country: Portugal Institution/Affiliation country: Centro Hospitalar Universitário do Porto/PT