Tratamento endovascular de aneurisma sacular aórtico associado à doença de Adamantiades-Behçet / Endovascular treatment of aortic saccular aneurysms associated with Adamantiades-Behçet disease
J. vasc. bras
;
20: e20200201, 2021. tab, graf
Article
in Portuguese
| LILACS
| ID: biblio-1279369
RESUMO
Resumo A doença de Adamantiades-Behçet é uma desordem multissistêmica que se apresenta classicamente com úlceras orais e genitais e envolvimento ocular, podendo o acometimento vascular ocorrer em até 38% dos casos. O envolvimento aórtico é uma das manifestações mais severas e está associado a altas taxas de mortalidade, ocorrendo em 1,5 a 2,7% dos casos. Relatamos um caso de aneurisma sacular de aorta abdominal em um paciente de 49 anos com doença de Adamantiades-Behçet complicada, tratada por correção endovascular.
ABSTRACT
Abstract Adamantiades-Behçet disease is a multisystemic disorder that classically presents with oral and genital ulcers and ocular involvement, with vascular involvement in up to 38% of cases. Aortic involvement is one of the most serious manifestations and is associated with high mortality rates, occurring in 1.5 to 2.7% of cases. We report a case of a saccular abdominal aorta aneurysm in a 49-year-old male patient with complicated Adamantiades-Behçet disease that was treated with endovascular repair.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Aorta, Abdominal
/
Aortic Aneurysm
/
Behcet Syndrome
/
Endovascular Procedures
Type of study:
Risk factors
Limits:
Humans
/
Male
Language:
Portuguese
Journal:
J. vasc. bras
Journal subject:
Cardiology
Year:
2021
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Escola Bahiana de Medicina e Saúde Pública/BR
/
Hospital Geral Roberto Santos/BR
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