Pseudotumor retroperitoneal como apresentação de doença relacionada à IgG 4: relato de caso / Retroperitoneal pseudotumor as a presentation of IgG4-related disease: a case report
Rev. Soc. Bras. Clín. Méd
;
17(4): 194-197, dez 2019.
Article
in Portuguese
| LILACS
| ID: biblio-1284250
RESUMO
Apresentamos um caso de doença relacionada à IgG4 devido às suas várias formas de apresentação clínica e dificuldades diagnósticas, objetivando acrescentar à literatura científica essa apresentação atípica. Trata-se de um homem de 65 anos com dor abdominal, febre e sintomas urinários. Exames laboratoriais inocentes para processo infeccioso agudo. Em tomografia computadorizada de abdome, evidenciou-se pseudotumor em região retroperitoneal, envolvendo ureter, veia e artéria ilíacas. Foi submetido à ressecção cirúrgica, tendo sido confirmado o diagnóstico de doença relacionada à IgG4 pela imuno-histoquímica. Iniciou tratamento com glicocorticoide com melhora clínica importante, seguindo em acompanhamento ambulatorial.
ABSTRACT
This is a case report of IgG4-related disease because of its wide variety of clinical presentations and difficulties in diagnosis, aiming at adding this atypical presentation to scientific literature. It is a case of a 65-year-old man with abdominal pain, fever and urinary symptoms. Laboratory tests were naive for acute infectious processes. In a computed tomography of the abdomen, retroperitoneal pseudotumor involving ureter, and iliac vein and artery was found. The patient underwent surgical resection, and the diagnosis of IgG4-related disease was confirmed by immunohistochemistry. The treatment was begun with glucocorticoids, with important clinical improvement. He was followed in outpatient settings.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Retroperitoneal Neoplasms
/
Immunoglobulin G4-Related Disease
Limits:
Aged
/
Humans
/
Male
Language:
Portuguese
Journal:
Rev. Soc. Bras. Clín. Méd
Journal subject:
Therapeutics
Year:
2019
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Faculdades Integradas Pitágoras/BR
/
Hospital Universitário Clemente de Faria/BR
/
Santa Casa de Montes Claros/BR
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