An autopsy series of an oft-missed ante-mortem diagnosis: hemophagocytic lymphohistiocytosis
Autops. Case Rep
;
11: e2021243, 2021. tab, graf
Article
in English
| LILACS
| ID: biblio-1285402
ABSTRACT
Hemophagocytic lymphohistiocytosis (HLH) is a rare and potentially fatal syndrome resulting from a hyperactivated immune system. Diverse patient profiles and clinical presentations often result in misdiagnosis. This article describes the varied clinical presentations and autopsy findings in three patients with this entity. The etiopathogenesis of HLH, its disparate and confounding clinical features, the diagnostic criteria, and management principles are also briefly reviewed.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Lymphohistiocytosis, Hemophagocytic
Type of study:
Diagnostic study
Limits:
Adult
/
Humans
/
Male
Language:
English
Journal:
Autops. Case Rep
Journal subject:
Anatomia
/
Patologia Cl¡nica
/
Patologia Legal
Year:
2021
Type:
Article
Affiliation country:
India
Institution/Affiliation country:
Armed Forces Medical College and Command Hospital/IN
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