Síndrome de Mazabraud: reporte de un caso / Mazabraud syndrome: A case report
Rev. Asoc. Argent. Ortop. Traumatol
;
86(3): 365-374, 2021.
Article
in Spanish
| LILACS, BINACIS
| ID: biblio-1353933
RESUMEN
El síndrome de Mazabraud es una rara asociación de lesiones del sistema musculoesquelético. Resulta de la combinación de uno o varios mixomas intramusculares y displasia fibrosa. Presentamos a un hombre de 46 años con lesiones óseas compatibles con displasia fibrosa asociada a mixoma intramuscular configurando un síndrome de Mazabraud y una revisión de la bibliografía. Nivel de Evidencia IV
ABSTRACT
Mazabraud's Syndrome is a rare association of lesions to the musculoskeletal system. It results from the combination of one or more intramuscular myxomas and fibrous dysplasia. We present a case of a 46-year-old man with bone lesions compatible with fibrous dysplasia associated with intramuscular myxoma, configuring Mazabraud's Syndrome and a review of the literature. Level of Evidence IV
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Muscle Neoplasms
/
Fibrous Dysplasia of Bone
/
Myxoma
Language:
Spanish
Journal:
Rev. Asoc. Argent. Ortop. Traumatol
Journal subject:
Orthopedics
Year:
2021
Type:
Article
Affiliation country:
Argentina
Institution/Affiliation country:
Sanatorio Allende/AR
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