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Síndrome de Mazabraud: reporte de un caso / Mazabraud syndrome: A case report
Re, Rodrigo; Negri, Maximiliano; Flores, Jorge.
  • Re, Rodrigo; Sanatorio Allende. Servicio de Diagnóstico por Imágenes. Córdoba. AR
  • Negri, Maximiliano; Sanatorio Allende. Servicio de Ortopedia y Traumatología. Córdoba. AR
  • Flores, Jorge; Sanatorio Allende. Servicio de Anatomía Patológica. Córdoba. AR
Article in Spanish | LILACS, BINACIS | ID: biblio-1353933
RESUMEN
El síndrome de Mazabraud es una rara asociación de lesiones del sistema musculoesquelético. Resulta de la combinación de uno o varios mixomas intramusculares y displasia fibrosa. Presentamos a un hombre de 46 años con lesiones óseas compatibles con displasia fibrosa asociada a mixoma intramuscular configurando un síndrome de Mazabraud y una revisión de la bibliografía. Nivel de Evidencia IV
ABSTRACT
Mazabraud's Syndrome is a rare association of lesions to the musculoskeletal system. It results from the combination of one or more intramuscular myxomas and fibrous dysplasia. We present a case of a 46-year-old man with bone lesions compatible with fibrous dysplasia associated with intramuscular myxoma, configuring Mazabraud's Syndrome and a review of the literature. Level of Evidence IV
Subject(s)

Full text: Available Index: LILACS (Americas) Main subject: Muscle Neoplasms / Fibrous Dysplasia of Bone / Myxoma Language: Spanish Journal: Rev. Asoc. Argent. Ortop. Traumatol Journal subject: Orthopedics Year: 2021 Type: Article Affiliation country: Argentina Institution/Affiliation country: Sanatorio Allende/AR

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Full text: Available Index: LILACS (Americas) Main subject: Muscle Neoplasms / Fibrous Dysplasia of Bone / Myxoma Language: Spanish Journal: Rev. Asoc. Argent. Ortop. Traumatol Journal subject: Orthopedics Year: 2021 Type: Article Affiliation country: Argentina Institution/Affiliation country: Sanatorio Allende/AR