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Vasculite leucocitoclástica secundária a mieloma múltiplo / Leukocytoclastic vasculitis secondary to multiple myeloma
Rev. Assoc. Méd. Rio Gd. do Sul ; 65(2): 01022105, Abr. - Jun. 2021.
Article in Portuguese | LILACS | ID: biblio-1369011
RESUMO
RESUMO As vasculites são um grupo heterogêneo de manifestações clínicas que podem ser idiopáticas ou secundárias a outras desordens. As principais causas de vasculite secundária são as infecções e medicamentos. No entanto, em alguns casos, elas podem ser secundárias a neoplasias, particularmente as neoplasias hematológicas. A vasculite leucocitoclástica é a forma mais comum de vasculite cutânea associada a distúrbios linfoproliferativos². É apresentado caso de homem caucasoide de 53 anos com história de lesões vasculares dolorosas em extremidades de surgimento recente. Realizada investigação complementar, o paciente apresentou exames compatíveis com mieloma de células plasmocitárias e vasculite leucocitoclástica cutânea. Descartando-se os demais diagnósticos diferenciais, foi, então, firmado o diagnóstico de vasculite leucocitoclástica cutânea associada ao mieloma múltiplo. PALAVRAS-CHAVE Púrpura, vasculite leucocitoclástica secundária, mieloma múltiplo
ABSTRACT
ABSTRACT Vasculitis is a heterogeneous group of clinical manifestations that can be idiopathic or secondary to other disorders. The main causes of secondary vasculitis are infections and medications. However, in some cases, they can be secondary to neoplasms, particularly hematologic neoplasms. Leukocytoclastic vasculitis is the most common form of cutaneous vasculitis associated with lymphoproliferative disorders². We present the case of a 53-year-old Caucasian male with a history of recent onset of painful vascular lesions in the extremities. After further investigation, the patient presented tests compatible with plasma cell myeloma and cutaneous leukocytoclastic vasculitis. Discarding the other differential diagnoses, the diagnosis of cutaneous leukocytoclastic vasculitis associated with multiple myeloma was then established. KEYWORDS Purpura, secondary leukocytoclastic vasculitis, multiple myeloma
Subject(s)
Full text: Available Index: LILACS (Americas) Main subject: Purpura / Vasculitis, Leukocytoclastic, Cutaneous / Multiple Myeloma Limits: Humans Language: Portuguese Journal: Rev. Assoc. Méd. Rio Gd. do Sul Year: 2021 Type: Article Affiliation country: Brazil Institution/Affiliation country: Universidade Federal de Ciências da Saúde de Porto Alegre (UFCSPA)/BR

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Full text: Available Index: LILACS (Americas) Main subject: Purpura / Vasculitis, Leukocytoclastic, Cutaneous / Multiple Myeloma Limits: Humans Language: Portuguese Journal: Rev. Assoc. Méd. Rio Gd. do Sul Year: 2021 Type: Article Affiliation country: Brazil Institution/Affiliation country: Universidade Federal de Ciências da Saúde de Porto Alegre (UFCSPA)/BR