Coexistence of Straatsma syndrome without macular extension and abnormal ellipsoid zone / Coexistência da síndrome de Straatsma sem extensão macular e zona elipsoide anormal
Rev. bras. oftalmol
;
81: e0038, 2022. graf
Article
in English
| LILACS
| ID: biblio-1376777
ABSTRACT
ABSTRACT Myelinated retinal nerve fibers are rare congenital anomalies that appear as gray-white patches. They may be present in a syndrome characterized by ipsilateral myelinated retinal nerve fibers, myopia and amblyopia. The author reported an ellipsoid zone defect on spectral domain optical coherence tomography in a case of Straatsma syndrome without macular extension.
RESUMO
RESUMO Fibras nervosas retinais mielinizadas são anomalias congênitas raras que aparecem como manchas branco-acinzentadas. Eles podem se apresentar em uma síndrome caracterizada por fibras nervosas retinais mielinizadas ipsilaterais, miopia e ambliopia. O autor relatou um defeito na zona elipsoide na tomografia de coerência óptica de domínio espectral em um caso de síndrome de Straatsma sem extensão macular.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Retinal Diseases
/
Nerve Fibers
/
Nerve Fibers, Myelinated
Limits:
Adolescent
/
Female
/
Humans
Language:
English
Journal:
Rev. bras. oftalmol
Journal subject:
Ophthalmology
Year:
2022
Type:
Article
Affiliation country:
Turkey
Institution/Affiliation country:
Hakkari State Hospital/TR
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