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Neuraxial block anesthetic technique in a patient with SCN8A encephalopathy: case report
Machado, Eric Guimarães; Billé, Isis da Rocha Costa; Araújo, Mariana Moraes Pereira das Neves; Neves, José Francisco Nunes Pereira das; Maués, Gilson Lorena; Marcos, Marco Felipe Bouzada; Araújo, Fernando de Paiva.
  • Machado, Eric Guimarães; Santa Casa de Misericórdia de Juiz de Fora. Serviço de Anestesiologia. Juiz de Fora. BR
  • Billé, Isis da Rocha Costa; Santa Casa de Misericórdia de Juiz de Fora. Serviço de Anestesiologia. Juiz de Fora. BR
  • Araújo, Mariana Moraes Pereira das Neves; Hospital Monte Sinai. Serviço de Anestesiologia. Juiz de Fora. BR
  • Neves, José Francisco Nunes Pereira das; Hospital Monte Sinai. Serviço de Anestesiologia. Juiz de Fora. BR
  • Maués, Gilson Lorena; Hospital Monte Sinai. Serviço de Anestesiologia. Juiz de Fora. BR
  • Marcos, Marco Felipe Bouzada; Hospital Escola Luiz Gioseffi Jannuzzi. Valença. BR
  • Araújo, Fernando de Paiva; Hospital Monte Sinai. Serviço de Anestesiologia. Juiz de Fora. BR
Braz. J. Anesth. (Impr.) ; 72(6): 826-828, Nov.-Dec. 2022.
Article in English | LILACS | ID: biblio-1420612
ABSTRACT
Abstract Mutations in SCN8A gene lead to changes in sodium channels in the brain, which are correlated with severe epileptic syndrome. Due to the rarity, there are few studies that support anesthesia in that population. The present study aims to report alternatives to inhalation anesthesia at epileptic encephalopathy. Case report Male, 4 years old, with SCN8A encephalopathy with surgical indication of orchidopexy. Neuroaxis block was performed and dexmedetomidine was used as a pre-anesthetic and sedation. The anestheticsurgical act was uneventful.

Conclusion:

The association of neuraxial block and dexmedetomidine proved to be a viable alternative for surgery in patients with SCN8A encephalopathy.
Subject(s)


Full text: Available Index: LILACS (Americas) Main subject: Dexmedetomidine / Epilepsy / Anesthetics Limits: Child, preschool / Humans / Male Language: English Journal: Braz. J. Anesth. (Impr.) Year: 2022 Type: Article Affiliation country: Brazil Institution/Affiliation country: Hospital Escola Luiz Gioseffi Jannuzzi/BR / Hospital Monte Sinai/BR / Santa Casa de Misericórdia de Juiz de Fora/BR

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Full text: Available Index: LILACS (Americas) Main subject: Dexmedetomidine / Epilepsy / Anesthetics Limits: Child, preschool / Humans / Male Language: English Journal: Braz. J. Anesth. (Impr.) Year: 2022 Type: Article Affiliation country: Brazil Institution/Affiliation country: Hospital Escola Luiz Gioseffi Jannuzzi/BR / Hospital Monte Sinai/BR / Santa Casa de Misericórdia de Juiz de Fora/BR