Cardiac involvement in Erdheim-Chester disease: a case report
Clin. biomed. res
;
34(4): 406-409, 2014. ilus
Article
in English
| LILACS
| ID: biblio-834475
ABSTRACT
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tissue lesions to life-threatening systemic involvement. Although the initial descriptions published by Jakob Erdheim and William Chester in 1930 included a patient with right atrial infiltration on autopsy, cardiovascular involvement in ECD has only gained more recognition recently. In the present report, we describe a case with cardiac involvement, presenting with symptomatic heart failure and a cardiac mass assessed with echocardiogram and cardiac magnetic resonance imaging.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Echocardiography
/
Erdheim-Chester Disease
/
Heart Failure
Limits:
Female
/
Humans
Language:
English
Journal:
Clin. biomed. res
Journal subject:
Medicine
Year:
2014
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Hospital de Clínicas de Porto Alegre/BR
Similar
MEDLINE
...
LILACS
LIS