Melanoma intracraneal primario en un paciente adulto con melanosis neurocut nea / Primary intracranial melanoma in an adult patient with neurocutaneous melanosis
Rev. neuro-psiquiatr. (Impr.)
;
79(4): 277-281, oct.-dic. 2016. ilus
Article
in Spanish
| LILACS, LIPECS
| ID: biblio-836268
RESUMEN
La melanosis neurocutánea es un desorden congénito de escasa frecuencia, caracterizado por nevos cutáneoscongénitos y compromiso del sistema nervioso central. Ocurre más comúnmente durante la infancia y rara vez en laedad adulta. Se presenta el caso de un hombre de 30 años de edad con melanosis neurocutánea que luego desarrolla melanoma intracraneal. En conjunción con los hallazgos del examen físico de la piel, la resonancia magnéticanuclear juega un rol crucial en el diagnóstico de esta entidad clínica.
ABSTRACT
Neurocutaneous melanosis is a rare congenital disorder characterized by congenital cutaneous nevi and furtherinvolvement of the central nervous system. It occurs most commonly during childhood and rarely in adulthood.An unusual case of a 30-year-old man with neurocutaneous melanosis and subsequent intracranial melanoma, is presented. In conjunction with the skin findings of the physical examination, magnetic resonance imaging plays acrucial role in making the diagnosis of this clinical entity.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Neurocutaneous Syndromes
/
Melanoma
/
Melanosis
Limits:
Adult
/
Humans
/
Male
Language:
Spanish
Journal:
Rev. neuro-psiquiatr. (Impr.)
Year:
2016
Type:
Article
Institution/Affiliation country:
Hospital Luis Negreiros Vega/PE
/
Hospital Nacional Edgardo Rebagliati Martins/PE
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