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Síndrome POEMS: Comunicación de cuatro casos / POEMS syndrome. A report of four cases
Andresik, Diego; Russo, M Paula.
  • Andresik, Diego; Hospital Italiano de Buenos Aires. Servicio de Clínica Médica. AR
  • Russo, M Paula; Hospital Italiano de Buenos Aires. Servicio de Clínica Médica. AR
Medicina (B.Aires) ; 75(5): 324-327, Oct. 2015. tab
Article in Spanish | LILACS | ID: biblio-841522
RESUMEN
Se presentan cuatro casos de un raro síndrome paraneoplásico de una discrasia de células plamáticas compuesto por polineuropatía, organomegalia, endocrinopatía, banda monoclonal y lesiones cutáneas (POEMS). El objetivo de la comunicación de esta serie es alertar sobre diferentes formas de presentación del síndrome de POEMS para disminuir el tiempo de diagnóstico, ya que el tratamiento temprano reduce las secuelas y mejora la calidad de vida a largo plazo; también, señalar la importancia de la clasificación de la enfermedad hematológica para realizar el tratamiento específico.
ABSTRACT
Four cases of a rare paraneoplastic syndrome associated to a plasmatic cell disorder with polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin lesions (POEMS) are here reported. The purpose of the communication is to warn of different forms of presentation of POEMS syndrome to decrease the time of diagnosis, because early treatment reduces sequels and improves quality of life in the long term, also to remark the importance of classifying the hematological disease for specific treatment.
Subject(s)

Full text: Available Index: LILACS (Americas) Main subject: POEMS Syndrome / Glucocorticoids Limits: Adult / Aged / Female / Humans / Male Language: Spanish Journal: Medicina (B.Aires) Journal subject: Medicine Year: 2015 Type: Article Affiliation country: Argentina Institution/Affiliation country: Hospital Italiano de Buenos Aires/AR

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Full text: Available Index: LILACS (Americas) Main subject: POEMS Syndrome / Glucocorticoids Limits: Adult / Aged / Female / Humans / Male Language: Spanish Journal: Medicina (B.Aires) Journal subject: Medicine Year: 2015 Type: Article Affiliation country: Argentina Institution/Affiliation country: Hospital Italiano de Buenos Aires/AR