Mucinosis folicular primaria: presentación de un caso clínico tratado con tacrolimus unguënto al 0.1% / Primary follicular mucinosis: a case report treated with tacrolimus ointment 0.1 %

RESUMEN

La mucinosis folicular se caracteriza por depósito anómalo de mucina, en los folículos pilosos y glándulas sebáceas. Puede corresponder a un trastorno idiopático benigno y auto-limitado, especialmente en niños o representar un cuadro secundario a un trastorno mielo-proliferativo, generalmente un linfoma cutáneo-T. Presentamos el caso de una niña de diez años de edad, con varias placas eritemato-blanquecinas circulares, ocasionalmente pruriginosas, en cara, cuello y tronco, además de alopecia difusa de cinco meses de evolución. No hay ataque al estado general. El estudio histopatológico reportó un cuadro compatible con mucinosis folicular.

ABSTRACT

Follicular mucinosis is characterized by mucin deposits within the hair follicles and sebaceous glands. It can occur as a primary idiopathic benign disorder; it can; or it can arise as a secondary symptom of a malignant disorder, most commonly mycosis fungoide. Youth and localization in a single area used to be regarded as indicative of the benign nature of follicular mucinosis. We report the case of a ten years old girl who presented with a five months history of a multiple, slightly pruritic, erythematous patches on her face, neck and chest. Different local treatments were ineffective. Overall, she was healthy. Histopathological examination of the lesion showed the typical histological picture of follicular mucinosis.