Amiloidose cardíaca: relato de caso / Cardiac cmyloidosis: case report
Medicina (Ribeiräo Preto)
;
50(2): 123-129, mar.-abr. 2017. ilus
Article
in Portuguese
| LILACS
| ID: biblio-879873
RESUMO
A amiloidose é resultante do depósito extracelular de proteínas séricas (amiloide) e pode acometer quase todos os órgãos. A amiloidose cardíaca é uma cardiomiopatia geralmente progressiva que apresenta prognóstico reservado. Neste relato apresentamos um paciente com sinais e sintomas de insuficiência cardíaca e hipertrofia ventricular esquerda, que devido ao diagnóstico tardio de amiloidose cardíaca, acabou evoluindo a óbito. Assim, esta doença deve ser sempre considerada na ausência de outra causa que justifique tais achados. (AU)
ABSTRACT
Amyloidosis is a result of the extracellular deposit of seric proteins (amyloid) and almost all organs can be compromised. Cardiac amyloidosis is usually a progressive cardiomyopathy that has a bad prognosis. We present here a case report about a patient that had signs and symptoms of heart failure and left ventricle hypertrophy. Because it was not possible to make the diagnosis of cardiac amyloidosis in time, he died. This disease must be considered when no other cause for those findings exists. (AU)
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Signs and Symptoms
/
Heart Failure
/
Amyloid
Type of study:
Prognostic study
Limits:
Aged
/
Humans
/
Male
Language:
Portuguese
Journal:
Medicina (Ribeiräo Preto)
Journal subject:
Medicine
Year:
2017
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Hospital de Transplantes Euryclides de Jesus Zerbini/BR
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