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Tricodisplasia espinulosa asociada a síndrome mielodisplásico e inmunosupresión / Trichodysplasia spinulosa: report of one case
Navarrete-Dechent, Cristián; Cevallos, Carolina; Manríquez, Juan Jorge; Salazar, Claudio; González, Sergio.
  • Navarrete-Dechent, Cristián; Pontificia Universidad Católica de Chile. Facultad de Medicina. Departamento de Dermatología. Santiago. CL
  • Cevallos, Carolina; Pontificia Universidad Católica de Chile. Facultad de Medicina. Departamento de Dermatología. Santiago. CL
  • Manríquez, Juan Jorge; Pontificia Universidad Católica de Chile. Facultad de Medicina. Departamento de Dermatología. Santiago. CL
  • Salazar, Claudio; Pontificia Universidad Católica de Chile. Facultad de Medicina. Departamento de Dermatología. Santiago. CL
  • González, Sergio; Pontificia Universidad Católica de Chile. Facultad de Medicina. Departamento de Dermatología. Santiago. CL
Rev. méd. Chile ; 146(1): 107-110, ene. 2018. graf
Article in Spanish | LILACS | ID: biblio-902627
ABSTRACT
Trichodysplasia spinulosa is a rare disease that occurs in the setting of immunosuppression, associated with tolerogenic therapy used in allograft recipients or patients with hematologic malignancies. Clinically, it is characterized by a centrofacial cutaneous eruption of erythematous papules with a central keratinous spicule, often associated with variable degrees of alopecia. Histologic findings are characteristic, and electron microscopy reveals the presence of trichodysplasia spinulosa associated polyomavirus. We report a 47-year-old woman with idiopathic autoimmune pancytopenia refractory to diverse immunosuppressant regimens, with clinical and pathologic findings compatible with the disease, in whom complementary studies were required to exclude other differential diagnoses.
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Full text: Available Index: LILACS (Americas) Main subject: Facial Dermatoses / Mucormycosis Limits: Female / Humans Language: Spanish Journal: Rev. méd. Chile Journal subject: Medicine Year: 2018 Type: Article Affiliation country: Chile Institution/Affiliation country: Pontificia Universidad Católica de Chile/CL

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Full text: Available Index: LILACS (Americas) Main subject: Facial Dermatoses / Mucormycosis Limits: Female / Humans Language: Spanish Journal: Rev. méd. Chile Journal subject: Medicine Year: 2018 Type: Article Affiliation country: Chile Institution/Affiliation country: Pontificia Universidad Católica de Chile/CL