Your browser doesn't support javascript.
loading
Endobronchial solitary fibrous tumor
Oliveira, Cristiano Claudino; de Moraes, Marcelo Padovani Toledo; Colby, Thomas; Oliveira, Gilmar Felisberto; Hasimoto, Erica Nishida; Cataneo, Daniele Cristina; Cataneo, Antônio José Maria; De Faveri, Julio.
  • Oliveira, Cristiano Claudino; Universidade Estadual Paulista "Julio de Mesquita Filho". Botucatu School of Medicine. Department of Pathology. Botucatu. BR
  • de Moraes, Marcelo Padovani Toledo; Universidade Estadual Paulista "Julio de Mesquita Filho". Botucatu School of Medicine. Department of Pathology. Botucatu. BR
  • Colby, Thomas; Mayo Clinic. Department of Laboratory Medicine and Pathology. Phoenix. US
  • Oliveira, Gilmar Felisberto; Universidade Estadual Paulista "Julio de Mesquita Filho". Botucatu School of Medicine. Department of Surgery and Orthopedics. Botucatu. BR
  • Hasimoto, Erica Nishida; Universidade Estadual Paulista "Julio de Mesquita Filho". Botucatu School of Medicine. Department of Surgery and Orthopedics. Botucatu. BR
  • Cataneo, Daniele Cristina; Universidade Estadual Paulista "Julio de Mesquita Filho". Botucatu School of Medicine. Department of Surgery and Orthopedics. Botucatu. BR
  • Cataneo, Antônio José Maria; Universidade Estadual Paulista "Julio de Mesquita Filho". Botucatu School of Medicine. Department of Surgery and Orthopedics. Botucatu. BR
  • De Faveri, Julio; Universidade Estadual Paulista "Julio de Mesquita Filho". Botucatu School of Medicine. Department of Pathology. Botucatu. BR
Autops. Case Rep ; 6(4): 35-40, Oct.-Dec. 2016. ilus
Article in English | LILACS | ID: biblio-905088
ABSTRACT
Solitary fibrous tumor (SFT) is a mesenchymal neoplasm that appears primarily in the pleura and rarely in intrapulmonary or endobronchial topography. The authors report the case of a 47-year-old woman who presented obstructive respiratory symptoms for 4 years. The chest computed tomography and bronchoscopy showed an obstructive polypoid lesion located between the trachea and the left main bronchus associated with distal atelectasis of the left lung. A resection of the lesion was performed and, macroscopically, the mass was oval, encapsulated, and firm, measuring 2.3 × 1.7 × 1.5 cm. Histology revealed low-grade mesenchymal spindle cell neoplasm, with alternating cellularity, myxoid areas, and mature adipose tissue outbreaks, as well as blood vessels with irregular walls. The immunohistochemical study was positive for CD34, CD99, and BCL2. The diagnosis was SFT in an unusual topography. The patient's symptoms remitted after tumor excision, and no systemic problems were evident. SFTs primarily affect adults and often follow a benign course; however, their behavior is unpredictable. The presence of necrosis and mitotic activity may portend a poor prognosis. Endobronchial SFTs are rare but should be evaluated and monitored similar to SFTs at other sites, with a long-term follow-up
Subject(s)


Full text: Available Index: LILACS (Americas) Main subject: Bronchial Neoplasms / Solitary Fibrous Tumors Type of study: Prognostic study Limits: Female / Humans Language: English Journal: Autops. Case Rep Journal subject: Anatomia / Patologia Cl¡nica / Patologia Legal Year: 2016 Type: Article Affiliation country: Brazil / United States Institution/Affiliation country: Mayo Clinic/US / Universidade Estadual Paulista "Julio de Mesquita Filho"/BR

Similar

MEDLINE

...
LILACS

LIS


Full text: Available Index: LILACS (Americas) Main subject: Bronchial Neoplasms / Solitary Fibrous Tumors Type of study: Prognostic study Limits: Female / Humans Language: English Journal: Autops. Case Rep Journal subject: Anatomia / Patologia Cl¡nica / Patologia Legal Year: 2016 Type: Article Affiliation country: Brazil / United States Institution/Affiliation country: Mayo Clinic/US / Universidade Estadual Paulista "Julio de Mesquita Filho"/BR