Anetodermia primaria asociada a lupus eritematoso sistémico. A propósito de un caso / Associated primary anemia to systemic lupus erythematosus About a case
Arch. argent. dermatol
;
66(4): 108-118, jul. ago. 2016. ilus
Article
in Spanish
| LILACS
| ID: biblio-916160
RESUMEN
La anetodermia es un trastorno elastolítico infrecuente, caracterizado clínicamente por áreas de piel laxa y pérdida o disminución de las fibras elásticas en la histología. Este hallazgo sin enfermedad cutánea previa es conocido como anetodermia primaria y se suele asociar a enfermedades autoinmunes; dentro de éstas el lupus eritematoso sistémico (LES), con anticuerpos antifosfolipídicos, y el síndrome antifosfolipídico (SAF) son las más frecuentes. Presentamos una paciente con anetodermia primaria, LES y anticuerpos antifosfolipídicos positivos sin clínica de SAF (AU)
ABSTRACT
Anetoderma is an infrequent elastolytic disorder, clinically characterized by areas with lack of the skin and decreased elastic fibers at histology. This finding without previous skin disease is known as primary anetoderma and is often associated with autoimmune diseases such as systemic lupus erythematosus (SLE), with antiphospholipid antibodies, and antiphospholipid syndrome (APS). A female patient with primary anetoderma, SLE and positive antiphospholipid antibodies without clinical APS is reported (AU)
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Anetoderma
/
Lupus Erythematosus, Systemic
Type of study:
Risk factors
Limits:
Adult
/
Female
/
Humans
Language:
Spanish
Journal:
Arch. argent. dermatol
Journal subject:
Dermatology
Year:
2016
Type:
Article
Affiliation country:
Argentina
Institution/Affiliation country:
Hospital Bernardino Rivadavia/AR
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