Glaucoma in phacomatosis pigmentovascularis type II B associated with sturge-weber syndrome

ABSTRACT

We report a 28-year-old lady with phacomatosis pigmentovascularis type lib associated with Sturge-Weber syndrome, with ocular evidence of both conditions. Phacomatosis pigmentovascularis type lib is a rare condition characterized by coexistence of naevus flammeus and pigmentary naevi. This is the second phacomatosis pigmentovascularis and the first glaucoma case associated with phacomatosis pigmentovascularis described in Saudi Arabia