Neonatal erythematous lupus and atrioventricular block A case with a review of the teratum bed

ABSTRACT

Neonatal lupus erythematosus is a rare syndrome. It is characterized by a transient lupus dermatitis and congenital heart block. The immunopathogenesis of the disease has been linked to the presence of the SSA antibody. In this report we describe a symptomatic congenital heart block in a year old male whose mother had documented systemic lupus erythematosus. We also discuss how to manage a woman with lupus erythematosus and positive antiSSA/Ro antibodies. We conclude that patients with neonatal lupus and their mothers shold be observed closely before delivery and for prolonged periods for signs of active disease