[Bilateral hemorrhagic renal angiomyolipoma. Case report and review of the literature]

ABSTRACT

Renal angiomyolipoma is a rare benign tumor representing 0.3% of renal tumors. In its bilateral from it is frequently part of a hereditary syndrome, such as tuberous sclerosis of Bourneville [TSB]. We report the case of a 32-year-old who has been followed up for TSB since 1995. In April 2004 she was hospitalized after several episodes of total hematuria with blood clots in the bladder causing severe exsanguination and the need for repeated blood transfusions. Serum creatinine was normal. Ultrasound and CT scan showed the presence of bilateral renal angiomyolipomas. The bleeding could be controlled by arterial embolization of the right kidney. One month later, the patient was admitted again with massive hematuria and hemorrhagic shock, and right nephrectomy was done to achieve hemostasis. The follow-up period of 24 months has been uneventful