Primary pulmonary rhabdomyosarcoma

ABSTRACT

Rhabdomyosarcoma is the commonest soft tissue malignancy in children; its common sites of occurrence include head and neck regions, chest wall, abdomen, perineal and anal regions. Lung is an unusual site. We report a case of two years old female child who presented with fever cough, shortness of breath and chest pain. Radiological examination showed a bullous lesion in the left lower lobe. Histological examination of bullectomy specimen revealed sheets and clusters of round blue cells with mild to moderate atypia. There were some hypocellular areas containing characteristic perivascular arrangement of tumour cells. Tumor cells showed strong positivity for Desmin. Based on histopathological and immunostain findings, diagnosis of Embryonal Rhabdomyosarcoma was made