Two unusual tumours in a patient of xeroderma pigmentosum: angiosarcoma and basosquamous carcinoma

ABSTRACT

Xeroderma pigmentosum [XP] is a rare form of genodermatosis, characterized by cutaneous pigmentary changes, sensitivity to light and development of multiple cutaneous and internal malignancies at an early age as a result of nucleotide excision repair defect after ultraviolet light exposure. Cutaneous angiosarcomas are angry neoplasms that are rarely associated with XP. In this communication, we report the case of a 22-year-old male patient with XP who developed an angiosarcoma of the face and a basosquamous carcinoma at one time. It is probably the first such case reported from Pakistan